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Bone dysplasia in Hutchinson-Gilford progeria syndrome is associated with dysregulated differentiation and function of bone cell populations.
Cabral, Wayne A; Stephan, Chris; Terajima, Masahiko; Thaivalappil, Abhirami A; Blanchard, Owen; Tavarez, Urraca L; Narisu, Narisu; Yan, Tingfen; Wincovitch, Stephen M; Taga, Yuki; Yamauchi, Mitsuo; Kozloff, Kenneth M; Erdos, Michael R; Collins, Francis S.
Affiliation
  • Cabral WA; Molecular Genetics Section, Center for Precision Health Research, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Stephan C; Departments of Orthopedic Surgery and Biomedical Engineering, University of Michigan, Ann Arbor, Michigan, USA.
  • Terajima M; Division of Oral and Craniofacial Health Sciences, Adams School of Dentistry, University of North Carolina, Chapel Hill, North Carolina, USA.
  • Thaivalappil AA; Molecular Genetics Section, Center for Precision Health Research, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Blanchard O; Departments of Orthopedic Surgery and Biomedical Engineering, University of Michigan, Ann Arbor, Michigan, USA.
  • Tavarez UL; Molecular Genetics Section, Center for Precision Health Research, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Narisu N; Molecular Genetics Section, Center for Precision Health Research, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Yan T; Molecular Genetics Section, Center for Precision Health Research, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Wincovitch SM; Cytogenetics and Microscopy Core, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Taga Y; Nippi Research Institute of Biomatrix, Ibaraki, Japan.
  • Yamauchi M; Division of Oral and Craniofacial Health Sciences, Adams School of Dentistry, University of North Carolina, Chapel Hill, North Carolina, USA.
  • Kozloff KM; Departments of Orthopedic Surgery and Biomedical Engineering, University of Michigan, Ann Arbor, Michigan, USA.
  • Erdos MR; Molecular Genetics Section, Center for Precision Health Research, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
  • Collins FS; Molecular Genetics Section, Center for Precision Health Research, National Human Genome Research Institute, NIH, Bethesda, Maryland, USA.
Aging Cell ; 22(9): e13903, 2023 09.
Article in En | MEDLINE | ID: mdl-37365004

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Progeria / Bone Diseases, Developmental / Aging, Premature Type of study: Prognostic_studies / Risk_factors_studies Limits: Animals Language: En Journal: Aging Cell Year: 2023 Type: Article Affiliation country: United States

Full text: 1 Collection: 01-internacional Database: MEDLINE Main subject: Progeria / Bone Diseases, Developmental / Aging, Premature Type of study: Prognostic_studies / Risk_factors_studies Limits: Animals Language: En Journal: Aging Cell Year: 2023 Type: Article Affiliation country: United States