Anesthesia management in a child with mucopolysaccharidosis and toxic epidermal necrolysis: A case report.
Paediatr Anaesth
; 34(1): 89-91, 2024 01.
Article
in En
| MEDLINE
| ID: mdl-37577929
ABSTRACT
Toxic epidermal necrolysis and mucopolysaccharidosis are both rare diseases that pose significant airway maintenance challenges to anesthesiologists. In this report, we describe the anesthesia management in a 4-year-old male with mucopolysaccharidosis type II who developed toxic epidermal necrolysis and presented for ophthalmic surgical procedures. Combined use of propofol and ketamine with the support of high-flow nasal oxygen enabled adequate analgesia and sedation while maintaining spontaneous ventilation and airway patency. The strategy presented in this report may contribute to enhancing the safety of sedation in spontaneously breathing children with abnormal airways.
Key words
Full text:
1
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Propofol
/
Stevens-Johnson Syndrome
/
Mucopolysaccharidosis II
/
Anesthesia
/
Ketamine
Limits:
Child
/
Child, preschool
/
Humans
/
Male
Language:
En
Journal:
Paediatr Anaesth
Journal subject:
ANESTESIOLOGIA
/
PEDIATRIA
Year:
2024
Type:
Article
Affiliation country:
Japan