Primary biliary cirrhosis and myopathy: an uncommon association
Rev. Hosp. Clin. Fac. Med. Univ. Säo Paulo
; 54(5): 165-8, Sept.-Oct. 1999. ilus
Article
em En
| LILACS
| ID: lil-255573
Biblioteca responsável:
BR1.1
RESUMO
Primary biliary cirrhosis (PBC) is a cholestatic liver disease, which is characterized by a chronic inflammatory destruction of intrahepatic bile ducts. It is a rare disorder whose precise etiology is still to be elucidated. Even though the liver is the principal target of PBC, other organ systems also might be affected. Muscular involvement has rarely been described in this disease, and in the majority of cases, muscular weakness has been interpreted as polymyositis. We report the case of a 48-year-old woman suffering from classic PBC, in association with a myopathy whose histological features are distinct from the cases reported before. We also performed a MEDLINE research for PBC and concomitant muscular diseases
Texto completo:
1
Coleções:
01-internacional
Base de dados:
LILACS
Assunto principal:
Polimiosite
/
Cirrose Hepática Biliar
Tipo de estudo:
Diagnostic_studies
/
Risk_factors_studies
Limite:
Female
/
Humans
Idioma:
En
Revista:
Rev. Hosp. Clin. Fac. Med. Univ. Säo Paulo
Assunto da revista:
MEDICINA
Ano de publicação:
1999
Tipo de documento:
Article