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Genetic reduction of cilium length by targeting intraflagellar transport 88 protein impedes kidney and liver cyst formation in mouse models of autosomal polycystic kidney disease.
Shao, Lina; El-Jouni, Wassim; Kong, Fanwu; Ramesh, Janani; Kumar, Radhe Shantha; Shen, Xiaogang; Ren, Jingjing; Devendra, Shruti; Dorschel, Arianna; Wu, Maoqing; Barrera, Ivan; Tabari, Azadeh; Hu, Kang; Haque, Nadeem; Yambayev, Ilyas; Li, Shiqi; Kumar, Amresh; Behera, Tapas Ranjan; McDonough, Gregory; Furuichi, Masahito; Xifaras, Michael; Lu, Tzongshi; Alhayaza, Rami Mohammad; Miyabayashi, Koji; Fan, Qiuling; Ajay, Amrendra K; Zhou, Jing.
Afiliação
  • Shao L; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA; Nephrology Division, Zhejiang Provincial People's Hospital, Hangzhou, Zhejiang Province, China.
  • El-Jouni W; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA; Division of Nephrology, Department of Medicine, Massachusetts General Hospital, Boston, Massachusetts, USA.
  • Kong F; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Ramesh J; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Kumar RS; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Shen X; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA; Nephrology Division, Zhejiang Provincial People's Hospital, Hangzhou, Zhejiang Province, China.
  • Ren J; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA; Nephrology Division, Zhejiang Provincial People's Hospital, Hangzhou, Zhejiang Province, China.
  • Devendra S; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Dorschel A; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Wu M; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Barrera I; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Tabari A; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Hu K; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA; Nephrology Division, Zhejiang Provincial People's Hospital, Hangzhou, Zhejiang Province, China.
  • Haque N; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Yambayev I; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Li S; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Kumar A; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Behera TR; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • McDonough G; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Furuichi M; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Xifaras M; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Lu T; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Alhayaza RM; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Miyabayashi K; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Fan Q; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Ajay AK; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
  • Zhou J; Harvard Center for Polycystic Kidney Disease Research and Renal Division, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA. Electronic address: jzhou@bwh.harvard.edu.
Kidney Int ; 98(5): 1225-1241, 2020 11.
Article em En | MEDLINE | ID: mdl-32610050

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Rim Policístico Autossômico Dominante / Cistos / Doenças Renais Policísticas Tipo de estudo: Prognostic_studies Limite: Animals / Humans Idioma: En Revista: Kidney Int Ano de publicação: 2020 Tipo de documento: Article País de afiliação: China

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Rim Policístico Autossômico Dominante / Cistos / Doenças Renais Policísticas Tipo de estudo: Prognostic_studies Limite: Animals / Humans Idioma: En Revista: Kidney Int Ano de publicação: 2020 Tipo de documento: Article País de afiliação: China