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Ataxic phenotype and neurodegeneration are triggered by the impairment of chaperone-mediated autophagy in cerebellar neurons.
Sato, Masahiro; Ohta, Tomoko; Morikawa, Yuri; Konno, Ayumu; Hirai, Hirokazu; Kurauchi, Yuki; Hisatsune, Akinori; Katsuki, Hiroshi; Seki, Takahiro.
Afiliação
  • Sato M; Department of Chemico-Pharmacological Sciences, Graduate School of Pharmaceutical Sciences, Kumamoto University, Kumamoto, Japan.
  • Ohta T; Laboratory for Mechanistic Chemistry of Biomolecules, Department of Chemistry, Keio University, Yokohama, Japan.
  • Morikawa Y; Department of Chemico-Pharmacological Sciences, Graduate School of Pharmaceutical Sciences, Kumamoto University, Kumamoto, Japan.
  • Konno A; Department of Chemico-Pharmacological Sciences, Graduate School of Pharmaceutical Sciences, Kumamoto University, Kumamoto, Japan.
  • Hirai H; Department of Neurophysiology & Neural Repair, Gunma University Graduate School of Medicine, Maebashi, Japan.
  • Kurauchi Y; Department of Neurophysiology & Neural Repair, Gunma University Graduate School of Medicine, Maebashi, Japan.
  • Hisatsune A; Department of Chemico-Pharmacological Sciences, Graduate School of Pharmaceutical Sciences, Kumamoto University, Kumamoto, Japan.
  • Katsuki H; Department of Chemico-Pharmacological Sciences, Graduate School of Pharmaceutical Sciences, Kumamoto University, Kumamoto, Japan.
  • Seki T; Department of Chemico-Pharmacological Sciences, Graduate School of Pharmaceutical Sciences, Kumamoto University, Kumamoto, Japan.
Neuropathol Appl Neurobiol ; 47(2): 198-209, 2021 02.
Article em En | MEDLINE | ID: mdl-32722888

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Ataxia Cerebelar / Cerebelo / Proteína 2 de Membrana Associada ao Lisossomo / Autofagia Mediada por Chaperonas / Degeneração Neural / Neurônios Limite: Animals Idioma: En Revista: Neuropathol Appl Neurobiol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Japão

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Ataxia Cerebelar / Cerebelo / Proteína 2 de Membrana Associada ao Lisossomo / Autofagia Mediada por Chaperonas / Degeneração Neural / Neurônios Limite: Animals Idioma: En Revista: Neuropathol Appl Neurobiol Ano de publicação: 2021 Tipo de documento: Article País de afiliação: Japão