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Effects of Elexacaftor/Tezacaftor/Ivacaftor Therapy on Lung Clearance Index and Magnetic Resonance Imaging in Patients with Cystic Fibrosis and One or Two F508del Alleles.
Graeber, Simon Y; Renz, Diane M; Stahl, Mirjam; Pallenberg, Sophia T; Sommerburg, Olaf; Naehrlich, Lutz; Berges, Julian; Dohna, Martha; Ringshausen, Felix C; Doellinger, Felix; Vitzthum, Constanze; Röhmel, Jobst; Allomba, Christine; Hämmerling, Susanne; Barth, Sandra; Rückes-Nilges, Claudia; Wielpütz, Mark O; Hansen, Gesine; Vogel-Claussen, Jens; Tümmler, Burkhard; Mall, Marcus A; Dittrich, Anna-Maria.
Afiliação
  • Graeber SY; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, and Cystic Fibrosis Center, and.
  • Renz DM; Berlin Institute of Health at Charité - Universitätsmedizin Berlin, Berlin, Germany.
  • Stahl M; German Center for Lung Research (DZL), associated partner site, Berlin, Germany.
  • Pallenberg ST; Department for Radiology.
  • Sommerburg O; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, and Cystic Fibrosis Center, and.
  • Naehrlich L; Berlin Institute of Health at Charité - Universitätsmedizin Berlin, Berlin, Germany.
  • Berges J; German Center for Lung Research (DZL), associated partner site, Berlin, Germany.
  • Dohna M; Department for Pediatric Pneumology, Allergology, and Neonatology.
  • Ringshausen FC; German Center for Lung Research, Biomedical Research in Endstage and Obstructive Lung Disease (BREATH).
  • Doellinger F; Division of Pediatric Pulmonology and Allergy and Cystic Fibrosis Center, Department of Pediatrics.
  • Vitzthum C; Department of Translational Pulmonology, Translational Lung Research Center Heidelberg (TLRC), German Center for Lung Research (DZL), and.
  • Röhmel J; Department of Pediatrics, Justus-Liebig-University Giessen, Giessen, Germany; and.
  • Allomba C; Universities of Giessen and Marburg Lung Center (UGMLC), German Center for Lung Research (DZL), Giessen, Germany.
  • Hämmerling S; Division of Pediatric Pulmonology and Allergy and Cystic Fibrosis Center, Department of Pediatrics.
  • Barth S; Department of Translational Pulmonology, Translational Lung Research Center Heidelberg (TLRC), German Center for Lung Research (DZL), and.
  • Rückes-Nilges C; Department for Radiology.
  • Wielpütz MO; German Center for Lung Research, Biomedical Research in Endstage and Obstructive Lung Disease (BREATH).
  • Hansen G; Department for Pneumology, and.
  • Vogel-Claussen J; Department of Radiology, Charité - Universitätsmedizin Berlin, corporate member of Freie Universität Berlin and Humboldt-Universität zu Berlin, Berlin, Germany.
  • Tümmler B; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, and Cystic Fibrosis Center, and.
  • Mall MA; German Center for Lung Research (DZL), associated partner site, Berlin, Germany.
  • Dittrich AM; Department of Pediatric Respiratory Medicine, Immunology and Critical Care Medicine, and Cystic Fibrosis Center, and.
Am J Respir Crit Care Med ; 206(3): 311-320, 2022 08 01.
Article em En | MEDLINE | ID: mdl-35536314

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Regulador de Condutância Transmembrana em Fibrose Cística / Fibrose Cística Tipo de estudo: Clinical_trials / Observational_studies Limite: Adolescent / Adult / Aged / Humans Idioma: En Revista: Am J Respir Crit Care Med Assunto da revista: TERAPIA INTENSIVA Ano de publicação: 2022 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Regulador de Condutância Transmembrana em Fibrose Cística / Fibrose Cística Tipo de estudo: Clinical_trials / Observational_studies Limite: Adolescent / Adult / Aged / Humans Idioma: En Revista: Am J Respir Crit Care Med Assunto da revista: TERAPIA INTENSIVA Ano de publicação: 2022 Tipo de documento: Article