RESUMEN
Involuntary upper right arm muscle contractions and spasms, which began intermittently when the patient was a teenager, were now a real problem for him as an adult. The patient was having difficulty rolling a baseball underhand to players as part of infield practice and he was experiencing muscle spasms when lifting his right arm over his head. "Twitches" in the patient's upper arm were making drinking difficult, but he had no problems feeding himself, writing, or performing other basic activities of daily living.
Asunto(s)
Distonía/diagnóstico , Distonía/tratamiento farmacológico , Músculos/fisiopatología , Hombro/fisiopatología , Espasmo/diagnóstico , Espasmo/tratamiento farmacológico , Espasmo/terapia , Adulto , Béisbol , Distonía/fisiopatología , Humanos , Masculino , Espasmo/fisiopatología , Resultado del TratamientoRESUMEN
Reversible cerebral vasoconstriction syndrome (RCVS) typically presents with recurrent thunderclap headaches and neurological deficits that are usually self-limiting. The intra-arterial (IA) use of vasodilators for RCVS has been reported for severe cases. Patients with RCVS have the potential for serious and permanent neurological deficits. It is a rare disorder, with a recent surge in the number of reports, and probably continues to be under-diagnosed. We report two patients with RCVS with severe neurological sequelae, treated in a large tertiary hospital. Both patients received high-dose cortico steroids due to the possibility of angiitis of the central nervous system, but they deteriorated neurologically, which suggests that steroids may have a deleterious effect in RCVS. Treatment with IA verapamil resulted in reversal of vasoconstriction, but multiple treatments were necessary. Therefore, IA administration of verapamil is a possible treatment for severe RCVS, but there is only limited sustained improvement in vasodilation that may require repetitive treatments with a currently undetermined optimal treatment interval.