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Lupus ; 21(4): 445-8, 2012 Apr.
Artículo en Inglés | MEDLINE | ID: mdl-21997967

RESUMEN

Protein-losing enteropathy is a rare manifestation of systemic lupus erythematosus. We report the case of an 18-year-old woman that presented initially with diarrhoea and anasarca. During evaluation, there was low serum albumin of 1.6 g/dl (3.5-5.2 g/dl) and a positive antinuclear antibody test (1:2560). Anti-Sm antibodies (ELISA) were positive in addition to low serum C3 of 35 mg/dl. A scintigraphy using 99mTc-labelled albumin was positive for abdominal protein loss. A diagnosis of systemic lupus erythematosus related protein-losing enteropathy was made. She was started on prednisolone 40 mg/day without amelioration; a month later, azathioprine (100 mg/day) was added, leading to normalization of serum albumin and resolution of symptoms within 4 months. After 1.5 years, the patient developed a 2.9 g 24-h proteinuria while still in remission of the protein-losing enteropathy, receiving 5 mg prednisone and 100 mg azathioprine daily.


Asunto(s)
Lupus Eritematoso Sistémico/complicaciones , Lupus Eritematoso Sistémico/diagnóstico , Enteropatías Perdedoras de Proteínas/diagnóstico , Enteropatías Perdedoras de Proteínas/etiología , Adolescente , Anticuerpos Antinucleares/sangre , Azatioprina/uso terapéutico , Biomarcadores/sangre , Complemento C3/análisis , Diarrea/etiología , Quimioterapia Combinada , Edema/etiología , Ensayo de Inmunoadsorción Enzimática , Femenino , Humanos , Hipoalbuminemia/etiología , Inmunosupresores/uso terapéutico , Lupus Eritematoso Sistémico/sangre , Lupus Eritematoso Sistémico/tratamiento farmacológico , Nefritis Lúpica/etiología , Prednisolona/uso terapéutico , Prednisona/uso terapéutico , Enteropatías Perdedoras de Proteínas/sangre , Enteropatías Perdedoras de Proteínas/tratamiento farmacológico , Proteinuria/etiología , Albúmina Sérica/análisis , Factores de Tiempo , Resultado del Tratamiento
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