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Paediatr Respir Rev
; 35: 93-94, 2020 Sep.
Artículo
en Inglés
| MEDLINE
| ID: mdl-32800451
RESUMEN
Cystic fibrosis liver disease (CFLD) affects a large proportion of cystic fibrosis (CF) patients; however encephalopathy is a rare complication. While classical hepatic encephalopathy can be a feature of end-stage liver disease, "hyperammonemic encephalopathy" can be precipitated in previously stable CFLD by various triggers including systemic corticosteroids. We describe one such case and review the relevant literature.