[Primary retroperitoneal synovial sarcoma revealed by hemorrhagic shock]. / Synovialosarcome rétropéritonéal révélé par un choc hémorragique.

INTRODUCTION: Primary retroperitoneal synovial sarcoma is a rare malignant neoplasm that typically arises in young adults. We report here an unusual presentation of this tumor during hemorrhagic shock and retroperitoneal hematoma. CASE: A 31-year-old man was admitted complaining of acute violent pain of the right lower abdominal quadrant. Physical examination was normal. The computed tomography scan showed a heterogeneous retroperitoneal mass near the iliac bifurcation, with a diameter of 3 cm and spontaneous contrast. The tumor ruptured shortly afterwards and the patient underwent emergency surgery for hemorrhagic shock and retroperitoneal hematoma. No metastases were observed. Although six cycles of doxorubicin and ifosfamide led to initial clinical and tomographic remission, relapse occurred 17 months later. DISCUSSION: Only 20 cases of primary retroperitoneal synovial sarcoma have been described. They are most often discovered following abdominal pain or anemia. Tumor rupture with retroperitoneal hematoma has not previously been reported. Surgical ablation remains the basis for management of this tumor, and survival appears to depend on its quality. Prognosis is poor. Our case is original by the tumor's location and mode of discovery.

[Spiegelian hernias. Report of 51 cases]. / Hernies ventrales antérolatérales dites de Spiegel. 51 cas.

We describe 51 cases of Spiegel's hernias, and report a critical review of the relevant literature. The patients presented with an isolated mass in 17 cases, abdominal pain in 17 cases, and a complication in 14 cases (intestinal occlusion in 8, incarceration in 6). The hernia was discovered fortuitously by compute tomography in three cases. The diagnosis was made preoperatively in 31 cases and during surgery in 17 cases. Sonography was contributory in 10 cases and compute tomography in 6 cases. In 47 cases the deep orifice was located at the level of Douglas' arch, in the anterolateral abdomen. The hernial sack remained interstitial in every case, under the aponeurosis of the external oblique. The contents were irreducible or strangulated in 14 cases. Surgery was necessary in all but three cases. The approach was lateral in 43 cases and medial in 5 cases. The indications of laparoscopy in this setting are discussed.