Generalized odontodysplasia in a 5-year-old patient with Hallermann-Streiff syndrome: clinical aspects, cone beam computed tomography findings, and conservative clinical approach.

This article aims to report the main clinical aspects, cone beam computed tomography (CBCT) findings, and conservative oral rehabilitation in a child born from a consanguineous marriage who presented with Hallermann-Streiff syndrome (HSS) and generalized odontodysplasia. A 5-year-old girl presented with a diagnosis of HSS for oral evaluation. Radiographically, all teeth showed wide pulp chambers and roots with thin dentinal walls and open apices, resembling ghost teeth and indicating a diagnosis of odontodysplasia. Oral rehabilitation consisted of partial dentures that were regularly adjusted to conform the device with the pattern of growth and development of the child. CBCT scan provided great insight into HSS, allowing a detailed view of the morphologic aspects and associated trabecular bone pattern. Treatment of these 2 rare conditions in young children must consider the stage of growth and development. Although extremely rare in HSS, odontodysplasia should be investigated and conservatively managed in young children.

[Dental anomalies in Chinese children with complete unilateral cleft lip and palate].

OBJECTIVE: To investigate the prevalence of dental anomalies in Chinese children with complete unilateral cleft lip and palate (UCLP). METHODS: Dental histories and radiographs of 244 Chinese children with UCLP were collected. The diagnosis of dental anomalies was based on panoramic radiographs before alveolar bone grafting. All patients were over 8 years old. RESULTS: In the UCLP group, 66.8% of the patients was presented with hypodontia. The maxillary lateral incisors were the most common teeth affected, followed by maxillary second premolars, mandibular incisors and mandibular second premolars. A total of 33.6% the patients was presented with dental malformation, most were microdontic laterel incisors. A total of 4.9% the patients was presented with hyperdontia. The supernumerary teeth were more frequently found in the cleft region. The prevalence of missing maxillary lateral incisor in the noncleft side was statistically different between genders, which was higher in male (P < 0.050). This group of Chinese children with UCLP demonstrated significantly higher prevalence of hypodontia, hyperdontia, and malformation on the cleft side than on the noncleft side (P < 0.01). CONCLUSIONS: Hypodontia is the most common type of dental anomalies. The prevalence of dental anomalies is higher in the UCLP patients than in the normal population. Dental anomalies occur more frequently on the cleft side than on the noncleft side.

Regional odontodysplasia involving three quadrants of the jaws: a case report.

Regional odontodysplasia is a rare developmental anomaly of the teeth that affects enamel and dentin. Its etiology is unknown, but the most accepted theory refers to circulatory disorders associated with vascular nevi. An uncommon case of regional odontodysplasia involving three quadrants of the jaws is reported. An 8-year-old boy was referred to the authors' institution with lack of teeth as a major symptom. There was no hereditary anomaly in the family. Extraoral examination revealed a brown discoloration on the skin on the right side of the face, neck, and chest. Detailed intraoral examination showed hypoplastic and carious teeth. Fistulae and gingival overgrowth were also observed. Radiographically, the affected teeth presented the pathognomonic image of "ghost teeth." Conservative treatment was instituted.

Regional odontodysplasia: report of a case in the mandible crossing the midline.

AIM: This report presents an unusual case of regional odontodysplasia (RO) in the mandible which crosses the midline along with its clinical management. BACKGROUND: RO is an uncommon, nonhereditary unilateral developmental anomaly involving the dental hard tissues, most frequently affecting the maxillary teeth. REPORT: RO was diagnosed in a 12-year-old. The dysplastic teeth were the mandibular canines, lateral incisors, central incisors, and the right premolars. The treatment was extraction of the affected teeth followed by provisory prosthetic rehabilitation. SUMMARY: The etiology of RO remains obscure. In this case a possible association with pre-natal trauma is suspected. The literature is not unanimous as to the management of RO. Nevertheless, the presence of a dental abscess is an indication for extraction. Since general bone quality is not affected, a provisory prosthesis was fabricated as the patient waits for future implant rehabilitation. The executed treatment met the expectations of the patient and her mother as it improved the patient's masticatory function, esthetics, and quality of life. CLINICAL SIGNIFICANCE: The general practitioner must be prepared to deal with different situations in the dental office. The diagnosis of RO relies mainly on clinical and radiographic findings, and its treatment depends on the affected teeth, the severity of the dysplasia, the presence of infection, and the patient's age.

Consideraciones clínicas de un caso de odontodisplasia regional / Clinical considerations of a regional odontodysplasia case

La odontodisplasia regional (RO) es una anomalía no hereditaria poco frecuente del desarrollo dentario, que afecta el componente ectodérmico y mesodérmico de las piezas dentarias, generalmente de un cuadrante y en forma unilateral. El diagnóstico y tratamiento de las anomalías dentales como ésta, constituye una de las áreas importantes de la odontopediatría. Caso clínico: paciente de género masculino de 4 años de edad, consulta por traumatismo de los incisivos temporales superiores izquierdos. Las radiografías oclusal, periapical y panorámica mostraron en el cuadrante superior izaquierdo indicios de restos radiculares de estos incisivos, así como una imagen normal del primer molar temporal y su sucesor; retardo en el desarrollo de los incisivos permanentes, y la imagen característica de diente fantasma en el segundo molar temporal y primer molar permanente. Se diagnostica odontodisplasia regional. El paciente se trató por 2 años con acciones preventivas, haciendo énfasis en el autocontrol de placa bacteriana y aplicaciones de fluoruros en forma tópica. El sector anterior se rehabilitó con prótesis removible, siendo controlado con examen clínico y radiográfico a la espera del tratamiento de ortodoncia e implantes osteointegrados al finalizar la etapa de desarrollo y crecimiento. Como conclusión, es importante conocer la patología para un temprano y correcto diagnóstico, suprimir el dolor y realizar acciones tendientes a conseguir una función adecuada, restablecer la estética y dimensión vertical, facilitando la planificación y desarrollo del tratamiento definitivo.

Diente fantasma (Odontodisplasia) / Ghost tooth (Odontodysplasia)

La odontodisplasia regional es una malformacion dentaria no usual. Los dientes afectados muestran una distintiva apariencia clinica, radiografica e histologica. Se presenta un caso clinico en un paciente pediatrico con un diente permanente odontodisplasico, y se realiza una amplia revision de la literatura de esta patologia.

Diente fantasma (Odontodisplasia) / Ghost tooth (Odontodysplasia)

La odontodisplasia regional es una malformacion dentaria no usual. Los dientes afectados muestran una distintiva apariencia clinica, radiografica e histologica. Se presenta un caso clinico en un paciente pediatrico con un diente permanente odontodisplasico, y se realiza una amplia revision de la literatura de esta patologia. (AU)

Odontodisplasia regional: reporte de un caso clínico / Regional odontodysplasia: report of a clinical case

La odontodisplasia regional es una rara anomalía del desarrollo dentario que afecta a todos los tejidos que componen la pieza dentaria. Tiene preferencia por el sexo femenino y se presenta generalmente en el maxilar superior, en forma unilateral, afectando a las piezas anteriores. Tiene una imagen radiográfica que se ha denominado como "diente fantasma", debido a la escasa radiopacidad del esmalte y dentina, y a la amplitud de la cámara pulpar y conductos radiculares. Su causa es idiopática y numerosas hipótesis sobre su etiología han sido propuestas, pero ninguna de ellas ha sido comprobada. Presentamos un caso clínico de un paciente de sexo femenino que tiene afectado el maxilar superior en el sector anterior, en el cual quedan ilustrados los signos clínicos y radiográficos de esta lesión y se establece el tratamiento

Impairment of molar tooth eruption caused by x-radiation.

The effect of x-radiation on erupting molars is presented. New born, 5 day old Wistar rats were locally irradiated in the molar area with doses of 20 Gy. They were killed in two groups, 30 and 60 days postirradiation respectively. Two other groups of non irradiated, age matched rats were killed at the given times. In addition a control group of 5 day old animals was also studied. Radiographic and histologic studies were performed. Odontoblastic atrophy, odontodysplasia, rootless formation, and ankylosis of tooth to bone by osteodentin formation with the resulting lack of tooth eruption were observed. The relation between the histologic alterations and tooth eruption is discussed.

Regional odontodysplasia: a bibliography.

Regional odontodysplasia is a localized disorder of tissues of dental origin resulting in characteristically bizarre clinical and radiographic appearances. It most commonly affects the maxillary anterior teeth of both the permanent and primary dentitions. The authors present a worldwide bibliography of reported cases and discuss the suggested theories regarding the condition's etiology. Although the majority of cases of regional odontodysplasia must be regarded as idiopathic, various developmental anomalies may produce identical changes in the teeth in one or more quadrants. A number of previously reported cases are also reconsidered with regard to their diagnosis and guidelines are suggested for the treatment of patients affected by regional odontodysplasia.

Odontodysplasia in a horse.

Weight loss, poor growth and dysphagia occurred in a young stallion with some teeth missing, and soft, discolored and/or deformed deciduous incisors, premolars and molars. At necropsy, permanent teeth sites were filled with yellow, gelatinous material. Clinical signs suggested fluorosis but laboratory findings did not confirm the diagnosis.

Unilateral odontodysplasia with ipsilateral hypoplasia of the mid-face. A case report.

A ten-year-and-1-month-old patient with regional odontodysplasia in the right maxilla is presented. The tooth malformation extended as far as the midline. The teeth 654321 + were markedly affected and exhibited a small indistinctly mineralized border with the 7 + being somewhat hypermineralized. The affected teeth in the respective quadrant had incomplete, retarded root formation. In addition, the patient had an obvious hypoplasia of the zygomatico-maxillary complex on the right. Ischaemia due to insufficient blood supply by the maxillary artery on the right is considered to be a possible cause of the disturbance described, and this is discussed.

Nature and frequency of dental changes in idiopathic hypoparathyroidism and pseudohypoparathyroidism.

Eleven patients with idiopathic hypoparathyroidism and pseudohypoparathyroidism were examined orally and medically. All patients had a history of tetanic and/or epileptic manifestations. Correspondingly, disturbances in the metabolism of calcium and phosphorus had been present in all. Dental anomalies were demonstrated in all patients but one. Enamel hypoplasia was observed in six cases, disturbances in tooth eruption in eight, root defects in five and hypodontia in seven. Dental anomalies were more frequent than could be expected from the literature, probably because the dental aspects of hypoparathyroid disease often have been overlooked. In the present material, the above-mentioned disturbances were most severe and frequent in the pseudohypoparathyroid group. Hypoparathyroid conditions are highly invalidating, easily accessible to treatment, but often undiagnosed for years. Therefore, the dental observation of severe disturbances in tooth formation and eruption pattern may be of crucial importance and should lead to further medical investigation.

Unilateral odontodysplasia.

A case of malformation of five permanent teeth in the right maxilla is described. The asymmetrical malformations were probably caused by an early local trauma of the right maxilla. This trauma led to defective mineralization of the deciduous tooth germs, which was verified roentgenologically. The resulting early osteitic process caused injury to the permanent germs at a sensitive mineralization period. Mineralization disturbances of 13, 14, 15, 16 and 17 were established roentgenologically. In the other halves of the jaws the development was entirely normal. Endocrinological examination showed normal values and there were no signs of hypothyreosis or Turner's syndrome. Acute symptoms in the right maxilla at the age of 9 necessitated extraction of germs 14 and 16. As subsequent roentgenograms showed that 13 and 15 were not developing normally in respect of mineralization, these were extracted at, respectively, 12 and 13 years of age. For the same reason 17 was extracted two years later. The histopathological examination showed in all involved teeth a pronounced malformation with disturbances both of the morpho- and histodifferentiation of the various dental tissues.