[Primary malignant solitary fibrous tumor/hemangiopericytoma of the parotid gland]. / Tumor fibroso solitario maligno primario/hemangiopericitoma de la glándula parótida

Solitary fibrous tumor (SFT) was first described in the pleura by Lietaud in 1767; later in 1870, Wagner described the localized nature of this type of tumor and Klemperer and Rabin classified pleural tumors into two types: diffuse mesotheliomas and localized mesotheliomas. Recent years have seen the redefinition of this neoplasm, due to better technology; it is now proven that this neoplasm may have multiple different extrapleural origins including the head and neck regions. This diversity of locations is related to the particular mesenchymal histogenesis of SFT which allows its development from very unusual sites such as the salivary glands (SGs). In this particular site, this neoplasm is very infrequent and most of reported cases refer to benign disease, with just one case informed so far of primary malignant SFT.

Peritoneal solitary fibrous tumour (SFT): long-term survival of recurrent and metastasised SFT treated with cytoreductive surgery and intraperitoneal chemotherapy.

This study reports a case of a SFT of the peritoneum in a 44-year-old white man that recurred 3 years after the initial surgical removal of the tumour. The patient recurred diffusely, developing a pattern of sarcomatosis and hepatic metastasis and was treated by surgical cytoreduction followed by intraoperative peritoneal hyperthermic chemotherapy (IPHC). Subsequently, he developed pulmonary metastases and was treated with palliative chemotherapy. The patient persisted with recurrent and distant disease, although it was reduced and stabilised, allowing his survival for the last 3 years since the extended surgery. New treatment strategies for a rare disease such as this one have first to be described in order to improve patient follow-up.