Synovial chondromatosis of the temporomandibular joint-clinical, surgical, and imaging findings of a Milgram stage III case series.

Synovial chondromatosis of the temporomandibular joint (TMJ) is a rare disease characterized by cartilaginous metaplasia of the mesenchymal remnants of the synovial membrane with formation of loose cartilaginous nodules. It is prevalent in middle-aged women and the main clinical characteristics are swelling, pain, and limited jaw movements. Diagnosis is difficult, especially in the early stages, because the signs and symptoms are like other TMJ diseases such as internal derangements and tumors. Imaging exams are fundamental in differential diagnosis for detection of synovitis and free cartilaginous bodies. Magnetic resonance imaging with a gadolinium contrast would be of particular interest for this purpose. Treatment involves the removal of the cartilaginous nodules and synovectomy. It can be performed by arthroscopy or arthrotomy depending on the size of the lesion, the number of corpuscles, and the need for auxiliary surgical procedures. Final diagnosis is anatomopathologic. Postoperative follow-up is necessary due to the risk of recurrence.

Luxación controlada de cadera en el tratamiento de la condromatosis sinovial asociada a una lesión tipo cam / Surgical hip dislocation for the treatment of synovial chondromatosis associated with a cam deformity

La condromatosis sinovial es una rara enfermedad benigna del tejido sinovial que puede causar daño articular si no se trata adecuadamente. Mientras que la lesión tipo cam provoca una fricción entre el borde acetabular y la unión cuello-cabeza femoral que puede generar un daño condrolabral y, en su evolución natural, llegar a la artrosis. El tratamiento de la condromatosis sinovial de cadera es controvertido, entre la cirugía abierta o artroscópica, pero debe incluir la extracción completa de los cuerpos libres y la sinovectomía para evitar recurrencias. Por el contrario, la lesión tipo cam puede manejarse con artroscopia en la mayoría de los casos. Presentamos un caso clínico en el que se asocian ambas patologías y que fue tratado mediante luxación controlada de cadera. La elección de la luxación controlada permite una visión completa de la articulación y se ha utilizado con éxito en casos de condromatosis sinovial asociada a la lesión tipo cam. Nivel de Evidencia: IV

Synovial chondromatosis is a rare benign disease of the synovial tissue that can cause joint damage if not properly treated. On the other hand, cam deformity causes friction between the acetabular rim and the femoral neck-head junction, which can lead to chondrolabral damage and, in its natural progression, result in osteoarthritis. The treatment of synovial chondromatosis of the hip is controversial, involving open surgery or arthroscopy, but it should include complete removal of loose bodies and synovectomy to prevent recurrences. In contrast, a cam lesion can often be managed with arthroscopy. We present a clinical case where both conditions were associated and treated with controlled hip dislocation. The choice of controlled dislocation allows for a comprehensive view of the joint and has been successfully used in cases of synovial chondromatosis associated with cam lesions. Level of Evidence: IV

Osteocondromatosis sinovial de hombro. Una enfermedad poco frecuente / Shoulder synovial osteocondromatosis. A rare disease

RESUMEN La osteocondromatosis sinovial es una condición poco común que se caracteriza por la formación de nódulos cartilaginosos u óseos comúnmente visto en las articulaciones sobretodo en la rodilla, sin embargo en el hombro esta condición es rara. Presentamos un caso clínico de una mujer de 35 años de edad con dolor en hombro izquierdo de larga evolución, tratado de manera conservadora antes de ser referido a un ortopedista. Luego de un diagnostico clínico y radiológico se sometió a tratamiento quirúrgico en la que se realizó un desbridamiento y escisión de los cuerpos condrales con éxito. Palabras claves: Condromatosis sinovial, tratamiento, adulto joven, mujer

ABSTRACTSynovial osteochondromatosis is a rare condition characterized by the formation of cartilage or bone nodules commonly seen in the joints, especially in the knee, however, this condition is rare in the shoulder. We present a clinical case of a 35-year-old woman with a long history of left shoulder pain, treated conservatively before being referred to an orthopedist. After a clinical and radiological diagnosis, she underwent surgical treatment in which a successful debridement and excision of the chondral bodies was performed

Osteocondromatosis sinovial de rodilla: una causa infrecuente de gonalgia en edad pediátrica / Synovial chondromatosis of the knee. A rare cause of knee pain in pediatric age

La osteocondromatosis sinovial es una metaplasia benigna de la membrana sinovial que afecta a 1 de cada 100 000 personas, en su mayoría adultos, y es extremadamente infrecuente en edad pediátrica. Predomina en grandes articulaciones, sobre todo la rodilla, y la sintomatología es, por lo general, inespecífica. Dado que la radiografía simple no suele ser concluyente, se recurre a la resonancia magnética nuclear y a la tomografía axial computarizada para orientar el diagnóstico. Se expone el caso de una paciente de 10 años de edad con gonalgia y dismorfia en la patela izquierda de seis meses de evolución, con diagnóstico de osteocondromatosis sinovial. Se presenta el caso dado que se trata de una entidad muy rara en niños, pero que requiere un tratamiento quirúrgico precoz para evitar sus posibles complicaciones, como la destrucción articular progresiva o la malignización a condrosarcoma.

Synovial osteochondromatosis consists of a synovial metaplasia which affects 1 per 100 000 people. It is a very rare disease among children. It typically affects large joints of the body, especially the knee. Due to the lack of specificity of the signs and symptoms and X-Ray images, imaging tests such as nuclear magnetic resonance or computerized tomography are frequently needed for diagnosis.We report a case of a ten-year-old female patient with a six months history of pain and deformity of left patella which was diagnosed with synovial osteochondromatosis. This case highlights the importance of clinical suspicion, not only because it is an extremely rare disease in children, but also because it needs a surgical treatment as soon as possible in order to avoid consequences it might have in pediatric age, as joint destruction or malignization to chondrosarcoma.

[Synovial chondromatosis of the knee. A rare cause of knee pain in pediatric age]. / Osteocondromatosis sinovial de rodilla: una causa infrecuente de gonalgia en edad pediátrica.

Synovial osteochondromatosis consists of a synovial metaplasia which affects 1 per 100 000 people. It is a very rare disease among children. It typically affects large joints of the body, especially the knee. Due to the lack of specificity of the signs and symptoms and X-Ray images, imaging tests such as nuclear magnetic resonance or computerized tomography are frequently needed for diagnosis. We report a case of a ten-year-old female patient with a six months history of pain and deformity of left patella which was diagnosed with synovial osteochondromatosis. This case highlights the importance of clinical suspicion, not only because it is an extremely rare disease in children, but also because it needs a surgical treatment as soon as possible in order to avoid consequences it might have in pediatric age, as joint destruction or malignization to chondrosarcoma.

La osteocondromatosis sinovial es una metaplasia benigna de la membrana sinovial que afecta a 1 de cada 100 000 personas, en su mayoría adultos, y es extremadamente infrecuente en edad pediátrica. Predomina en grandes articulaciones, sobre todo la rodilla, y la sintomatología es, por lo general, inespecífica. Dado que la radiografía simple no suele ser concluyente, se recurre a la resonancia magnética nuclear y a la tomografía axial computarizada para orientar el diagnóstico. Se expone el caso de una paciente de 10 años de edad con gonalgia y dismorfia en la patela izquierda de seis meses de evolución, con diagnóstico de osteocondromatosis sinovial. Se presenta el caso dado que se trata de una entidad muy rara en niños, pero que requiere un tratamiento quirúrgico precoz para evitar sus posibles complicaciones, como la destrucción articular progresiva o la malignización a condrosarcoma.

Surgical treatment of a rare bilateral synovial chondromatosis

Synovial chondromatosis (SC) in the temporomandibular joint (TMJ) is an uncommon entity, mostly when the involvement is bilateral. The authors report a rare case of bilateral SC, with a follow-up of 13 months, and a literature review. A 60-year-old Caucasian woman, with the chief complaint of pain for 6 years in the bilateral pre-auricular region, had a progressive clacking and discomfort on the left side during mouth opening. The panoramic image was suggestive of SC. The bilateral lesion was surgically removed by direct access. Histopathological examination confirmed the clinical diagnosis of bilateral SC. This article shows the importance of a multidisciplinary approach for the early diagnosis and appropriate treatment. Also, it encourages the referral of such cases to professionals with a greater familiarity with this entity.

Condromatosis Sinovial Primaria de la Articulación Temporomandibular con Extensión a Hueso Temporal. Reporte de un Caso y Revisión de la Literatura / Primary Synovial Chondromatosis of the Temporomandibular Joint with Temporal Bone Extension. Case Report and Literature Review

RESUMEN: La condromatosis sinovial (CS), es una lesión benigna poco frecuente y de clínica bastante inespecífica. Suele afectar articulaciones de huesos largos como la rodilla, el codo y la cadera, presentándose generalmente de manera unilateral. Se cree que solo un 3 % de los casos de CS afecta la articulación temporomandibular. Esta condición se caracteriza por ser un trastorno metaplásico del tejido conectivo sinovial que suele manifestarse con la formación de pequeños y múltiples nódulos de cartílago que posteriormente pueden desprenderse, calcificarse y formar cuerpos libres dentro del espacio articular. Presentamos el caso de una mujer de 55 años con condromatosis sinovial de la articulación temporomandibular, tratada desde hace 3 años bajo el diagnóstico de desórdenes temporomandibulares. A pesar de ser considerada una lesión de tipo benigna, esta puede llegar a ser localmente agresiva, extendiéndose como en nuestro reporte hacia la fosa craneal media, adelgazando parte del hueso temporal.

ABSTRACT: Synovial chondromatosis (CS) is a benign lesion that is rare and clinically quite nonspecific. It usually affects the joints of long bones such as the knee, elbow and hip, usually occurring unilaterally. It is believed that in only 3 % of cases of CS the temporomandibular joint. This is a condition its characterized by being a metaplastic synovial connective tissue that manifests itself with the formation of small and multiple cartridges that detach, calcify and form free bodies within the joint space. We present the case of a 55-year-old woman with synovial chondromatosis of the temporomandibular joint, treated for 3 years under the diagnosis of temporomandibular disorders. Despite being considered a benign lesion, this can become locally aggressive, extending as in our report to the cranial fossa, thinning part of the temporal bone.

Extensive Synovial Chondromatosis Involving All Flexor Tendons in the Tarsal Tunnel: A Case Report / Condromatose sinovial extensa envolvendo todos os tendões do túnel do tarso: relato de caso

Abstract Synovial chondromatosis is a rare condition characterized by benign chondrogenic metaplasia of extra-articular synovial tissue. It usually affects a single tendon sheath of the hand or foot. This report describes a rare case with extensive synovial chondromatosis affecting all flexor tendons in the tarsal tunnel, its radiological features, surgical treatment, and clinical outcome. The authors present a unique case of extensive synovial chondromatosis in a 48-year-old male involving the tendon sheaths of the flexor hallucis longus, flexor digitorum longus, and posterior tibialis tendons, at the level of the tarsal tunnel, with extension into the plantar aspect of the foot. The patient initially presentedwith symptoms of tarsal tunnel compression and was found to have a 4-cm mass in the posteromedial aspect of the ankle. The presumptive diagnosis of synovial chondromatosiswasmadebased on radiographic and magnetic resonance imaging evidence. The patient underwent surgical resection of the tumor, aswell as tarsal tunnel releaseandgastrocnemius recession. The diagnosiswas confirmed postoperatively by surgical histopathology. The postoperative course of the patient was uncomplicated and his tarsal tunnel symptoms resolved. This represents a case of extensive synovial chondromatosis involving all flexor tendons in the tarsal tunnel that was correctly diagnosed by clinical and imaging findings, which required early surgical resection to avoid long-term neurovascular complications.

Resumo A condromatose sinovial é uma condição rara caracterizada por metaplasia condrogênica benigna do tecido sinovial extra-articular, que geralmente afeta uma única bainha tendínea da mão ou do pé. O objetivo é relatar o caso raro de um paciente com diagnóstico de condromatose sinovial extensa afetando todos os tendões flexores na topografia do túnel do tarso, suas características radiológicas, tratamento cirúrgico e desfecho clínico. Os autores apresentam um caso único de condromatose sinovial extensa em um homem de 48 anos envolvendo as bainhas dos tendões flexor longo do hálux, flexor longo dos dedos e tibial posterior, na topografia do túnel do tarso, com extensão para a região plantar do retropé. O sintoma inicial foi de compressão neurovascular (síndrome do túnel do tarso). A suspeita diagnóstica foi condromatose sinovial com base em evidências radiográficas e de ressonância magnética. O paciente foi submetido a ressecção cirúrgica do tumor, bem como a liberação do túnel tarsal e alongamento do tendão dos gastrocnêmios. O diagnóstico foi confirmado por exame histopatológico do espécime colhido no período intraoperatório. A evolução pósoperatória do paciente ocorreu sem complicações e os sintomas da síndrome do túnel do tarso cessaram. Os autores relatam um caso de condromatose sinovial extensa envolvendo todos os tendões flexores do túnel do tarso, corretamente diagnosticado por achados clínicos e radiológicos e que necessitou de ressecção cirúrgica precoce para evitar complicações neurovasculares em longo prazo.

Presentación inusual de condromatosis sinovial de la rodilla: caso reportado / Unusual presentation of synovial chondromatosis of the knee. Case report

La condromatosis sinovial se caracteriza por la formación de múltiples nódulos cartilaginosos intraarticulares del tejido subsinovial, que puede ser diagnosticada erróneamente debido a la ausencia de un examen físico, o de hallazgos en RM característicos en etapas iniciales. Se presenta un caso de una mujer de 33 años que consulta por dolor, pseudobloqueo y contractura en flexión de rodilla izquierda sin antecedente traumático previo. Debido a la sospecha de condromatosis sinovial de rodilla, se indicó la exploración artroscópica. Intraoperatoriamente se identificaron múltiples cuerpos sueltos intra y extraarticulares cartilaginosos: se realizó una sinovectomía radical y extracción de cuerpos libres. Al año de seguimiento, el paciente recuperó el rango completo de movimiento y retornó íntegramente a la actividad deportiva. Los resultados del presente informe indican que, en casos en los que existe una sospecha de condromatosis sinovial, la exploración artroscópica es un método eficaz para el diagnóstico y tratamiento con resultados satisfactorios. Tipo de estudio: Reporte de caso. Nivel de evidencia: IV

We report an unusual presentation of synovial chondromatosis of the knee in a 33-year-old women. At this unusual age and location, there is a greater probability of missed diagnosis, due to the lack of definite informative incidence, and difficulty in finding the lesions. In this case, intra and extraarticular multiple loose bodies were hidden. After careful arthroscopic inspection, we found numerous cartilaginous loose bodies and removed them with arthroscopy in association with sinovectomy. Synovial chondromatosis, is a rare, benign condition characterized by the formation of multiple intraarticular cartilaginous nodules from the subsynovial tissue. Synovial chondromatosis can be often misdiagnosed due to the lack of a specific physical exam or MRI findings in early stages. The present report examines a 33-year-old female with symptoms of left knee flexion contracture, pain mechanical locking without previous traumatic event. Following admittance, an arthroscopic exploration was conducted. Multiple cartilage-like intra and extraarticular loose bodies were identified in the patient's joints during surgery. Radical synovectomy and removal of loose bodies were performed. Following one year follow-up, the patient recovered full range of motion and returned to sports activities. The results of the present report indicate that, in cases where synovial chondromatosis is suspected, arthroscopic exploration is an effective method for diagnosis and treatment with satisfactory results. Type of Study: Case report. Level of evidence: IV

Arthroscopic treatment of synovial chondromatosis of the ankle / Tratamento artroscópico de condromatose sinovial do tornozelo

ABSTRACT Synovial chondromatosis is a rare proliferative disease, characterized by the occurrence of metaplasia in the synovium of the joints. These lesions become pedunculated; with the evolution of the disease they become detached, leading to intra-articular loose-bodies. It occurs more frequently in males between the third and fifth decades of life, usually affecting large joints such as the knee and hip. Smaller joints, such as the ankle, are less frequently affected. Patients report articular pain, blockage, and limited range of motion caused by the loose fragments. As the disease progresses, the joint undergoes degenerative changes. This report describes a case of synovial chondromatosis of the ankle, treated by arthroscopy. The patient, a 59 year-old male, complained of pain and swelling of the left ankle. Physical evaluation showed limited tibiotarsal mobility (plantar flexion of 20° and dorsiflexion of 5°). After physical and imaging evaluation, the patient underwent ankle arthroscopy due to impingement of the joint, with limitation of mobility. Arthroscopic treatment allowed easy access to the joint, removal of loose bodies, and partial synovectomy, with low morbidity and early rehabilitation. The final prognosis was excellent.

RESUMO A condromatose sinovial é uma doença proliferativa, rara e caracterizada pela ocorrência de metaplasia na sinovial das articulações. Essas lesões tornam-se pediculadas e à medida que a doença evolui, as lesões se soltam, dão origem a corpos livres intra-articulares. A prevalência é maior em homens entre a terceira e quinta décadas de vida, atingindo normalmente grandes articulações como o joelho e o quadril. Articulações menores, como o tornozelo, são afetadas com menos frequência.Os pacientes referem dor articular, bloqueio e limitação da mobilidade causados pelos fragmentos livres. Com o evoluir da doença, a articulação sofre alterações degenerativas. Os autores apresentam um caso clínico de condromatose sinovial do tornozelo, tratado por artroscopia. O doente, do sexo masculino e de 59 anos, referia queixas de dor e edema do tornozelo esquerdo. Ao exame físico, apresentava limitação da mobilidade da tibiotársica (flexão plantar e dorsiflexão de 20° e 5°, respectivamente). Após avaliação clínica e estudo imagiológico, foi proposta artroscopia do tornozelo para tratamento de pinçamento articular com limitação da mobilidade. O tratamento artroscópico permitiu um fácil acesso à articulação, remoção dos corpos livres e sinovectomia parcial, com baixa morbilidade e reabilitação precoce. O prognóstico final foi excelente.

Bilateral symmetrical synovial chondromatosis of shoulder: a case report / Condromatose sinovial simétrica bilateral do ombro: relato de caso

ABSTRACT Synovial chondromatosis is a benign arthropathy rarely seen in diarthrodial joints. Extra-articular bilateral symmetrical synovial chondromatosis of shoulder is the rarest variety. The diagnosis is established with the help of imaging modalities and histopathological examinations. This report describes a case of a 39-year-old woman who presented with symmetrical, progressively increasing swelling over the bilateral shoulder region, of 12-18 months duration, with dull ache and restricted movements of the shoulder joints. Magnetic resonance imaging (MRI) and ultrasonography (USG) revealed large bilateral subacromial-subdeltoid bursal swelling with loose floating bodies. Surgical excision of extensive bilateral bursa was performed at four weeks of interval. Histopathological examination revealed synovial chondromatosis on either side. Postoperative recovery occurred without complications.

RESUMO A condromatose sinovial é uma artropatia benigna raramente vista em articulações diartrodiais. A condromatose sinovial simétrica bilateral extra-articular do ombro é a variedade mais rara. O diagnóstico é estabelecido com a ajuda de exames de imagem e histopatológicos. Este relato descreve o caso de uma paciente de 39 anos, com aumento de volume progressivo simétrico sobre a região bilateral do ombro com 12-18 meses de duração com dor entorpecido e limitação dos movimentos das articulações do ombro. A ressonância magnética e a ultrassonografia revelaram um grande aumento de volume da bursa subacromial subdeltoidea bilateral com corpos livres flutuantes. A excisão cirúrgica extensa da bursa bilateral foi feita com quatro semanas de intervalo. O exame histopatológico revelou condromatose sinovial em ambos os lados. A recuperação pós-operatória transcorreu sem complicações.

Lipoma sinovial com metaplasia condróide e osteóide mimetizando osteocondromatose sinovial em gato - relato de caso / Synovial limpoma with chondroid and osteoid metaplasiamimicking synovial osteochondromatosis in a cat

Lipomas são tumores de tecidos moles benignos um dos mais comuns e podem surgir de qualquer parte do corpo. As articulações não são locais de predileção para acontecer este tipo de neoplasia, entretanto na articulação femur-tíbio-patelar é descrito em humanos. A etiologia é desconhecida e o tratamento descrito é a remoção cirúrgica por artrotomia ou por artroscopia. Nós relatamos, pela primeira vez, a ocorrência desse tipo tumoral em um gato de 8 anos de idade cuja queixa principal era claudicação e à avaliação radiográfica foi sugerido ser osteocondromatose, o qual revelou ser uma metaplasia no de outra condição e, também para existência desse tipo tumoral como diagnóstico diferencial para claudicação.

Lipomas are one of the most common of all benign neoplasms of soft tissues, and althoughthey may arise almost anywhere in the body. The reports in human medicine shown the most affectedjoint in synovial lipomas is the knee joint and the etiology of this benign condition is unknown. Thetreatment described for synovial lipoma is surgical excision of the loose body by open arthrotomy orby arthroscopic guidance. We first described a case of a 8-year-old male domestic shorthair cat witha intermittent lameness presentation, whose it revealed to be a osteochodromatosis at radiographicstudy. Therefore, the histopathological examination revealed a to be synovial lipoma with osteoidand chondroid metaplastic tissue that have mimicked a osteochondromatisis radiographic lesion.This emphasizes the importance of histopathological evaluation and included this diagnosis inamong lameness in cats. (acompanhar a correção do resumo).

Lipoma sinovial com metaplasia condróide e osteóide mimetizando osteocondromatose sinovial em gato - relato de caso / Synovial limpoma with chondroid and osteoid metaplasiamimicking synovial osteochondromatosis in a cat

Lipomas são tumores de tecidos moles benignos um dos mais comuns e podem surgir de qualquer parte do corpo. As articulações não são locais de predileção para acontecer este tipo de neoplasia, entretanto na articulação femur-tíbio-patelar é descrito em humanos. A etiologia é desconhecida e o tratamento descrito é a remoção cirúrgica por artrotomia ou por artroscopia. Nós relatamos, pela primeira vez, a ocorrência desse tipo tumoral em um gato de 8 anos de idade cuja queixa principal era claudicação e à avaliação radiográfica foi sugerido ser osteocondromatose, o qual revelou ser uma metaplasia no de outra condição e, também para existência desse tipo tumoral como diagnóstico diferencial para claudicação.(AU)

Lipomas are one of the most common of all benign neoplasms of soft tissues, and althoughthey may arise almost anywhere in the body. The reports in human medicine shown the most affectedjoint in synovial lipomas is the knee joint and the etiology of this benign condition is unknown. Thetreatment described for synovial lipoma is surgical excision of the loose body by open arthrotomy orby arthroscopic guidance. We first described a case of a 8-year-old male domestic shorthair cat witha intermittent lameness presentation, whose it revealed to be a osteochodromatosis at radiographicstudy. Therefore, the histopathological examination revealed a to be synovial lipoma with osteoidand chondroid metaplastic tissue that have mimicked a osteochondromatisis radiographic lesion.This emphasizes the importance of histopathological evaluation and included this diagnosis inamong lameness in cats. (acompanhar a correção do resumo).(AU)

Synovial Chondromatosis of the Elbow With Asymptomatic Ulnar Nerve Compression.

Primary synovial chondromatosis is a rare, benign, proliferative disease of hyaline cartilaginous bodies within the synovium of joints. We report a rare case of primary synovial chondromatosis diffusely affecting the ulnohumeral joint causing pain and motion limitations with extrusion into the cubital tunnel and compressing the ulnar nerve but without any preoperative signs or symptoms of ulnar nerve compression. The patient was successfully treated with an open synovectomy to limit disease progression and improve motion. This case highlights that synovial conditions of the elbow may involve the ulnar nerve even when a patient is asymptomatic. Preoperative use of magnetic resonance imaging of the elbow should be considered in patients undergoing either an open or arthroscopic synovectomy.

Removal of a Solitary Synovial Chondromatosis of the Temporomandibular Joint Using Arthroscopy.

The diagnosis of synovial chrondromatosis of temporomandibular joint (TMJ) requires a combined assessment consisting of clinical, radiologic, and histopathologic examinations. The purpose of this study is to report in 1 patient the removal of a single large cartilaginous nodule floating in the upper joint compartment using arthroscopy. A 30-year-old woman was referred to our department complaining about pain in preauricular area and restricted mouth opening. Imaging of magnetic resonance reveals anterior disc displacement and right joint effusion. Arthroscopy of TMJ was performed for diagnosis and treatment. During the arthroscopy a large loose body was identified and removed with a biopsy forceps; lavage was conducted with ringer solution. Hyaluronic acid was injected in TMJ at surgery, 1 and 3 months after surgery. Postoperative magnetic resonance imaging showed articular disc on position and no effusion. The patient was followed up of 1 year without sign and symptoms. Arthroscopic procedure of TMJ was effective in diagnosis and removal of a solitary loose body of synovial chrondromatosis. Viscosupplementation appers to offer benefits in controlling pain and functional improvements.

Synovial Chondromatosis of the Knee in a 2-Year-Old Child: A Case Report and Review of the Literature.

CASE: We describe a rare case of synovial chondromatosis of the knee of a 2-year-old child. The diagnosis was based on the history, physical examination, and complementary examinations (radiography and magnetic resonance imaging). Anterior and posterior approaches were used for total synovectomy and resection of loose bodies. CONCLUSION: Physicians should keep this condition in mind, even in young children, because early identification prevents future secondary degenerative changes in the knee joint. As far as we know, this is the youngest child with synovial chondromatosis of the knee reported in the English-language literature.

Metotrexato en condromatosis sinovial: una serendipia / Methotrexate in sinovial chondromatosis: a case of serendipity

La condromatosis sinovial es una metaplasia idiopática benigna de la membrana sinovial que afecta a 1/100.000 habitantes, en una relación hombre/mujer de 3 a 1 entre los 30 y 50 años. Predomina en grandes articulaciones como rodilla (70%), cadera (20%) y hombro (19%), y en menor proporción en codo y tobillo. Puede ser primaria o secundaria. La etiología es desconocida. La resolución es quirúrgica ya sea por artroscopia o por cirugía a cielo abierto, no existiendo otra alternativa terapéutica. Se presenta el caso clínico de un paciente con condromatosis sinovial en hombro derecho, que se comporta como una artropatía erosiva, indicándose metotrexato y resolviendo casi totalmente los nódulos condromatosos.

The synovial chondromatosis is a benign idiopathic metaplasia ofthe synovial membrane which affects one in 100,000 inhabitants. Itis 3 times more common in males, aged between 30 and 50 yearsold. It is commonly found in large joints such as knee (70%), hip(20%) and shoulder (19%) and less frequently in elbow and heel. Itcan be primary or secondary. The etiology is still unknown.The resolution is surgical by means of arthroscopy or open surgery,existing no other therapeutic alternatives.We present a male patient with primary synovial chondromatosis inthe right shoulder, leading to an erosive arthropathy. Treatment withmethotrexate resolved almost entirely the cartilaginous nodules.

Bloqueo articular de codo por condromatosis sinovial: reporte de caso y revisión de literatura / Articular block of synovial chondromatosis of the elbow: case report and literature review

Introducción: La condromatosis sinovial es una patología benigna, infrecuente, de etiología desconocida en la que se desarrollauna metaplasia cartilaginosa del tejido sinovial. Se caracteriza por la formación de nódulos que son liberados en la cavidadarticular. El tratamiento consiste en la extracción de los cuerpos libres intraarticulares, preferentemente por vía artroscópica.Objetivo: reportar un caso de condromatosis sinovial de codo con bloqueo articular al que se le realizó extracción artroscópicade los cuerpos libres intraarticulares. Conjuntamente se efectuó una revisión bibliográfica de dicha infrecuente patología.Reporte de caso: Paciente masculino que presenta dolor, tumefacción, crepitación y limitación del rango de movimientoen flexo-extensión. En la radiografía se observan múltiples imágenes nodulares calcificadas en la cámara anterior yposterior del codo. En RMN y TAC se evidencian dichos nódulos depositados en las fosas olecraneana y coronoidea,asociados con cambios degenerativosarticulares. Se realiza extracción de los cuerpos libres intraarticulares ycapsulectomía parcial por vía artroscópica. Se confirma el diagnóstico de condromatosis sinovial por histopatología. En elpostoperatorio el paciente mejoró la sintomatología y aumentó el rango de flexo-extensión...

Introduction: Synovial chondromatosis is an infrequent, benign pathology of unknown etiology in which a cartilaginous metaplasia of synovial tissue develops. It is characterized by the formation of nodules that are released into the joint cavity. Treatment involves removal of intra-articular loose bodies, preferably arthroscopically. Objective: To report a case of synovial chondromatosis elbow joint to lock who underwent arthroscopic removal of intra-articular loose bodies. Together a literature review of this rare entity was made. Case report: Male patient has pain, swelling, crepitus and limitation of range of motion in flexion and extension. Multiple nodular radiographic images calcified in the anterior and posterior chamber elbow observed. MRI and CT in these nodules deposited in the olecranon and coronoid pits associated with degenerative articular changes are evident. Removal of intra-articular loose bodies and partial capsulectomy is performed arthroscopically. The diagnosis of synovial chondromatosis confirmed by histopathology. Postoperatively the patient improved symptoms and increased the range of flexion and extension...

Tratamiento artroscopico de la condromatosis sinovial en tobillo. reporte de caso y revision de la literatura / Arthroscopic treatment for synovial chondromatosis of the ankle. case report and literature review

La condromatosis sinovial es una enfermedad de etiología desconocida, poco frecuente, benigna, caracterizada por la formación de nódulos cartilaginosos metaplásicos dentro de la sinovial, bursa o vaina de tendones. Estos nódulos pueden desprenderse y convertirse en cuerpos libres dentro de la articulación. Afecta a los hombres dos veces más que las mujeres y, por lo general, ocurre entre la tercera y quinta década de la vida. Este proceso monoarticular afecta más comúnmente a la rodilla, seguido de la cadera, el codo, el hombro y tobillo. La afección extraarticular puede ocurrir si la proliferación de cuerpos libres rompen a través de la cápsula de la articulación o si las estructuras sinoviales fuera de la articulación (por ejemplo, vainas de los tendones, bursas) están involucradas. Se presenta un paciente de sexo masculino de 30 años de edad que acude por dolor en tobillo derecho, disminución del rango de movilidad y limitación progresiva para la deambulación de un año y medio de evolución. Al examen físico presentaba clínica de síndrome friccional anterior en tobillo, rango de movilidad limitado (flexión plantar 25º y dorsal 20º. No presenta antecedentes de inestabilidad previa ni comorbilidades. Con la presunción diagnóstica de condromatosis sinovial de tobillo se decidió llevar a cabo una artroscopia anterior de tobillo diagnóstica y terapéutica. Al año postoperatorio presentaba 30º de flexión plantar y 25º de flexión dorsal, sin dolor y sin recurrencia en las imágenes radiográficas. El escore del American Orthopaedic Foot and Ankle Society mejoro de 49 puntos en el preoperatorio a 97 puntos en el postoperatorio. En el caso presentado la artrosocopía permitió el tratamiento de la condromatosis sinovial de tobillo con buen resultado al año.

Synovial chondromatosis is an uncommon, benign disease of unknown etiology characterized by the formation of metaplastic cartilaginous nodes within the synovial bursa or tendon sheath. These nodules may break off and become free in the articular joint. It affects men twice more than women and usually occurs between the third and fifth decade of life. This monoarticular process most commonly affects the knee, followed by the hip, elbow, shoulder and ankle. The extra-articular condition can occur if the proliferation of loose bodies break through the joint capsule or synovial structures outside the joint (eg, tendon sheaths, bursae) are involved. We present a male patient of 30 years old who consulted for right ankle pain, decreased range of motion and progressive ambulation limitation for a year and a half of evolution. Physical examination showed clinical anterior impingement, limited dorsal and plantar flexion (25 and 20 degrees respectively), without instability. No history of relevance. With the suspected diagnosis of synovial chondromatosis it was decided to carry out a diagnostic and therapeutic arthroscopy of the ankle. At a year postoperative showed 30 degrees plantar flexion and 25 degrees of dorsiflexion, painlessly and without recurrence in radiographic images. The American orthopaedic foot and ankle society score improves from 49 in the preop to 97 in the postop. Arthroscopic treatment for ankle synovial chondromatosis provides acceptable improvement of clinical symptoms and range of motion at a year postop.