ABSTRACT
A 46-year-old female with profound sensorineural hearing loss in her left ear from childhood developed tinnitus and fluctuating hearing loss on the right side 8 years ago. Four years later, paroxysmal episodes of rotatory vertigo occurred with gradually increased frequency, lasting from half an hour to 2 hours and accompanied with nausea and vomiting. Audiometric test revealed severe sensorineural hearing loss in both of her ears. The tympanograms showed type A on both sides. The threshold of auditory brainstem response was 97 dBnHL in her right ear while no waves could be educed on her left side. Weakened right-sided vestibular function was confirmed on caloric testing and vestibular-evoked myogenic potential. A normal cochlear morphology and clearness cerebellopontine angle were shown in the MR imaging scan. She was diagnosed with Delayed Endolymphatic Hydrops.
Subject(s)
Cochlear Implantation , Endolymphatic Hydrops , Hearing Loss, Sensorineural/therapy , Semicircular Canals/pathology , Caloric Tests , Female , Humans , Middle Aged , VertigoABSTRACT
Objective:To analyze the clinical features of patients with facial nerve schwannoma to raise awareness of the disease and potential future treatments.Method: A series of 16 cases with facial nerve schwannoma were retrospective analyzed, including initial symptoms, medical and treatment history, imaging findings,surgical technique and outcome. Result: Ten cases of them were initially misdiagnosed: six cases as sudden facial paralysis,two as cholesteatoma and two as vestibular schwannomas.The diagnosis were revised after MRI examination for first eight cases, and other two patients were identified as the FNS after the surgery.Conclusion:MRI is a very valuable examination for the diagnosis of facial schwannoma,especially for patients with recurrent or progressive facial paresis,long term otorrhea with facial paresis. The possibility of atypical facial schwannoma should be considered for the patients with isolated internal auditory canal and cerebellopontine angle tumor presenting only auditory symptoms without facial nerve symptoms.