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Acta Myol ; 43(2): 78-82, 2024 Jun.
Article in English | MEDLINE | ID: mdl-39082325

ABSTRACT

Neuromuscular diseases (NMDs) comprise a heterogeneous group of conditions characterized by extreme progressive muscle weakness leading to respiratory failure. Noninvasive mechanical ventilation (NIV) has emerged as a cornerstone in the management of respiratory complications associated with NMDs. This review aims to elucidate the role of NMV in respiratory function, improving quality of life, and prolonging survival in individuals with NMD. The physiological basis of respiratory impairment in NMDs, principles of NMV application, evidence supporting its efficacy, patient selection criteria, and potential challenges in its application are discussed.


Subject(s)
Neuromuscular Diseases , Noninvasive Ventilation , Respiratory Insufficiency , Humans , Neuromuscular Diseases/physiopathology , Neuromuscular Diseases/therapy , Neuromuscular Diseases/complications , Noninvasive Ventilation/methods , Respiratory Insufficiency/therapy , Respiratory Insufficiency/etiology , Respiratory Insufficiency/physiopathology , Quality of Life
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