ABSTRACT
A case of a tentorial meningioma with atypical histological features invading the transverse sinus and extending along the internal jugular vein up to the superior mediastinum is described. This report illustrates one of the many ways meningiomas spread beyond the cranial cavity and the difficulty in managing such a problem.
Subject(s)
Magnetic Resonance Imaging , Mediastinum/diagnostic imaging , Mediastinum/pathology , Meningeal Neoplasms/diagnosis , Meningioma/diagnosis , Neoplasm Invasiveness/diagnosis , Tomography, X-Ray Computed , Adult , Craniotomy , Disease Progression , Female , Humans , Image Processing, Computer-Assisted , Jugular Veins/diagnostic imaging , Jugular Veins/pathology , Meningeal Neoplasms/surgery , Meningioma/surgery , Neurosurgical Procedures , Radiography, ThoracicABSTRACT
UNLABELLED: Sacral agenesis is an uncommon condition characterised by total or partial absence of the sacrum. The association of this condition with craniocervical junction abnormalities is extremely rare. CASE REPORT: We describe a 3-year-old girl who, at the age of 8 months, while being investigated for short stature, was found to have significant craniocervical instability associated with anomalies of the odontoid peg. In addition to this she had partial sacral agenesis but genetic tests showed a normal karyotype. Due to the inherent difficulty of surgical fixation and immobilisation in an infant of her age, she was managed conservatively in a soft cervical orthosis. At the age of three years, surgery for decompression and stabilisation was deemed necessary due to the onset of neurological morbidity. CONCLUSION: The authors describe this extremely rare association and discuss the difficulties faced while deciding the optimum surgical strategy for managing such young children with craniocervical instability.
Subject(s)
Abnormalities, Multiple/surgery , Atlanto-Axial Joint/abnormalities , Cervical Vertebrae/abnormalities , Joint Dislocations/congenital , Joint Instability/congenital , Nervous System Malformations/surgery , Odontoid Process/abnormalities , Sacrum/abnormalities , Spinal Fusion , Abnormalities, Multiple/diagnostic imaging , Atlanto-Axial Joint/pathology , Atlanto-Axial Joint/surgery , Bone Transplantation , Cervical Vertebrae/pathology , Cervical Vertebrae/surgery , Child, Preschool , Craniofacial Abnormalities/diagnosis , Decompression, Surgical , Female , Follow-Up Studies , Humans , Image Processing, Computer-Assisted , Infant , Joint Dislocations/diagnosis , Joint Dislocations/surgery , Joint Instability/diagnosis , Joint Instability/surgery , Magnetic Resonance Imaging , Nervous System Malformations/diagnosis , Occipital Bone/pathology , Occipital Bone/surgery , Odontoid Process/pathology , Odontoid Process/surgery , Sacrum/pathology , Spinal Cord Compression/diagnosis , Spinal Cord Compression/surgery , Tomography, X-Ray ComputedABSTRACT
The authors report a rare case of thoracic intradural extramedullary capillary haemangioma, the clinical presentation of which was similar to any other intraspinal mass. Magnetic resonance imaging does not always distinguish this entity from others, but the presence of enlarged vasculature is often a useful clue. Complete resection is the treatment of choice of this hamartomatous lesion.
