ABSTRACT
Congenital oculodermal melanocytosis represents a unilateral accumulation of melanocytes in the episclera, sclera and uveal tract. Clinically, it manifests with iris heterochromia, episcleral and scleral pigmented patches, dark pigmentation of the trabecular meshwork and the fundus. This congenital disorder is a predisposing factor for uveal melanoma and chronic glaucoma. We report here the case of a Caucasian woman who presents some of these characteristics.
La mélanocytose oculaire congénitale représente une accumulation unilatérale de mélanocytes au niveau de la sclère, l'épisclère et l'uvée. D'un point de vue clinique, on peut retrouver une hétérochromie irienne, une pigmentation de l'épisclère, de la sclère, du trabéculum et du fond d'Åil. Un risque majoré de mélanome uvéal et de glaucome chronique est retrouvé chez ces patients. Nous rapportons ici le cas d'une jeune patiente caucasienne qui présente certaines de ces caractéristiques cliniques de façon tout à fait asymptomatique.
Subject(s)
Melanoma , Melanosis , Nevus of Ota , Skin Neoplasms , Uveal Neoplasms , Female , Humans , Melanosis/diagnosis , Uveal Neoplasms/diagnosisABSTRACT
The blind from birth has a slower psychomotor development than the normal child because he must palliate the deficiency of visual information by the development of suppletory senses and integrate these information to the structuration of environment. An early assistance by a multidisciplinary team with an important participation of the family will however permit a harmonious development.
Subject(s)
Blindness/complications , Psychomotor Disorders/etiology , Adaptation, Physiological , Blindness/physiopathology , Child, Preschool , Humans , Infant , Psychomotor Disorders/physiopathology , Psychomotor PerformanceABSTRACT
Extracapsular cataract extraction (ECCE) was done in 35 eyes of 30 patients after previous retinal attachment surgery with scleral buckling. A posterior chamber intraocular lens (PC-IOL) was implanted in 35 eyes. No significant modification in the cataract surgical technique was necessary.
