Exuberant clear cell odontogenic carcinoma of the mandible harboring EWSR1 rearrangement: Report of a rare case and a literature review.

Clear cell odontogenic carcinoma (CCOC) is a rare malignant odontogenic tumour (MOT) that mainly affects the mandible, with a slight female predominance in adult patients. In this study, we described an exuberant CCOC in mandible of a 22-year-female patient. On radiographic examination, a radiolucent lesion in the region of tooth 36 to 44 with tooth displacement and alveolar cortical resorption was observed. Histopathological study revealed a malignant neoplasm of the odontogenic epithelium, composed of PAS-positive clear cells and immunoreactivity for CK5, CK7, CK19, p63. The Ki-67 index was low (<10 %). Fluorescent in situ hybridization revealed EWSR1 gene rearrangement. The diagnosis of CCOC was established and the patient was referred for surgical treatment.

Oral health in patients with Prader-Willi syndrome: current perspectives.

Prader-Willi syndrome (PWS) is a rare complex multisystem disorder and presents several aspects related to dentistry. The purpose of this review is to present current perspectives about oral health in patients with PWS. Delay development, hyperphagia, foamy and highly viscous saliva raise the risk of caries and contribute to tooth wear. Cariogenic foods uncontrolled consumption allows to obesity and dental problems progress worsening systemic disorders. These factors can be controlled. The success in follow-ups with caries free and oral health controlled demonstrate the importance of multidisciplinary team intervention corroborated by support at home from birth to adulthood. Thereby, current perspective on the disease is that there is possibility of proper maintenance of oral health in PWS patients. Guided care interferes positively with the overall well-being and quality of life of the individual with PWS and their family. A multidisciplinary team with a focus on teaching patients and family members will help minimize eventual problems.

Special Care Dentistry in a Patient with Prader-Willi Syndrome through the Use of Atraumatic Restorative Treatment under General Anesthesia.

Prader-Willi syndrome described in 1956 has a genetic origin, affecting both genders, varying in presence and intensity from individual to individual. A precocious diagnosis, before the manifestation of symptoms, has brought some improvement in the quality of life of the carriers in the last years. The objective of this case report was to describe the treatment realized in a 3-year-old boy who presented grade II obesity, difficulty of locomotion, hypotonia, and history of cardiopathy. A dental treatment under general anesthesia was defined, allowing an oral adequation in a single section, in which it was planned the extraction of the element 74 and atraumatic restorative treatment (ART) technique in the other teeth. The precocious intervention in this 3-year-old patient by the therapy realized with ART under general anesthesia was done with success, avoiding unnecessary extractions, preserving dental elements, and maintaining the oral cavity in adequate function.

Avaliação clínica periodontal em indivíduos portadores de síndrome de down / Periodontal clinical evaluation in individuals with Down Syndrome

A doença periodontal é causada por fatores etiológicos locais, especialmente o biofilme dentário, alguns tipos de distúrbios sistêmicos podem reduzir ou alterar a resposta do hospedeiro e, então, predispor a alterações periodontais. A dificuldade na escovação é um fator importante para o surgimento da doença periodontal em adolescentes com Síndrome de Down. O objetivo foi avaliar os parâmetros clínicos periodontais em indivíduos portadores de Síndrome de Down. Foram avaliados um total de 44 indivíduos de ambos os gêneros e faixa etária de 13 à 24 anos, 22 indivíduos apresentavam Síndrome de Down e 22 sem síndrome. Parâmetros periodontais como profundidade de sondagem, índice de placa e de sangramento foram mensurados. Os indivíduos foram divididos em dois grupos, grupo 1 com Síndrome de Down, média de idade de 17,8 anos e grupo 2 com indivíduos sem síndrome e com média de idade de 17,7 anos. O grupo 1 teve 2.17 mm de média de profundidade de sondagem, enquanto o grupo 2 teve média de 2,59 mm. Para o índice de placa, foi observada 31,8% dos indivíduos do grupo 1 enquanto no grupo 2 em 54,5%. Para o índice de sangramento a sondagem, observou-se que 40,9% dos indivíduos do grupo 1 tinham sangramento a sondagem e no grupo 2 59,1% apresentavam sangramento, com diferença estatística entre os grupos (p<0,05). Os indivíduos com Síndrome de Down apresentaram parâmetros clínicos periodontais compatíveis com saúde periodontal e quando comparados com indivíduos saudáveis não apresentam diferenças clinicas.

Periodontal disease is caused by local etiological factors, particularly the dental biofilm, some types of systemic disorders may reduce or alter the host response and then predisposes to periodontal changes. The difficulty in brushing is an important factor for the onset of periodontal disease in adolescents with Down syndrome. The objective was to evaluate the clinical periodontal parameters in individuals with Down syndrome. We evaluated a total of 44 individuals of both genders and aged 13 to 24 years, 22 subjects had Down syndrome and 22 without the syndrome. Periodontal parameters such as probing depth, plaque index and bleeding were measured. The subjects were divided into two groups, group 1 with Down Syndrome, mean age of 17.8 years and group 2 with individuals without the syndrome and with a mean age of 17.7 years. Group 1 was 2.17 mm average probing depth, while group 2 had a mean of 2.59 mm. For plaque index, it was observed 31.8% of subjects in Group 1 while in group 2 was 54.5%. For the survey bleeding index, it was observed that 40.9% of Group 1 subjects had bleeding on probing and group 2 59.1% had bleeding, with no statistical difference between the groups (p <0.05). We conclude that individuals with Down syndrome showed better gingival bleeding rates than those without dental syndrome by receiving periodic treatment in the educational institution they attend.

O exame inicial do paciente na clínica odontológica privada: metodologia e custos / The patient's initial exam in the private dental clinic: methodology and costs

A clínica médica tem o custo do exame inicial do paciente estabelecido e consagrado durante a efetivaçäo da consulta, mas a odontológica näo vivencia tal realidade. Todo o empenho dispensado durante a coleta de dados e toda a precisäo do diagnóstico näo säo devidamente valorizados, tanto pela populaçäo, quanto, principalmente, pela própria categoria profissional. Os chamados "orçamentos" säo realizados sem remuneraçäo. Em vista disso, este estudo tem o próposito de relatar o estado atual desse exame inicial. Para tanto, foram entrevistados cem profissionais de Araçatuba e regiäo, utilizando-se um questionário contendo perguntas relativas ao tipo de exame realizado e o que pensavam com relaçäo ao custo do mesmo...