[Complete atrioventricular block in Kearns-Sayre syndrome]. / Bloqueio atrioventricular total em síndrome de Kearns-Sayre.

A thirty-three year old woman, known to have Kearns-Sayre syndrome for eight years, had an ECG pattern of right bundle branch block and left anterior fascicular block that evolved to complete atrioventricular block, leading her to a syncopal episode. A temporary pacemaker and a permanent one were installed. The patient has been asymptomatic so far.