Hidatidosis of the spleen.

UNLABELLED: Hydatidosis of the spleen (SH) is an extremally rare condition. The aim of the study was to present our experience and discuss diagnostic methods and therapeutical options in cases of spleen hydatidosis. MATERIAL AND METHODS: Between 1993 and 2008, 8 patients were diagnosed with SH, 6 of whom were operated on (4 males and 2 females). Their average age was 44.5 years (the age range 30-59 years). Four patients presented isolated SH, one had a spleen and liver hydatidosis and there was also a case of one spleen, liver and peritoneal hydatidosis. RESULTS: The main symptom of the condition was abdominal pain and hydatidosis serology was always positive. The average hydatidisis cyst size was 13.3 cm (range: 7-18 cm). Splenectomy was performed in 5 cases and a partial cystectomy in one case. A left lateral sectionectomy was required in 1 case, a segment III subsegmentectomy was delivered in 1 case and multiple cystectomies in the case of the patient with disseminated hydatisis. In the follow-up period of the above mentioned surgical procedures no mortality among the treated patients was reported. The majority of patients did not present any symptoms of morbidity (4 patients). We registered one wound infection and one cavity abscess solved with percutaneous drainage in the patient following partial cystectomy. The hospitalisation period avaraged to 5 days (within the range of 5 to 12 days). The patients' follow-up was 98 months on average (range: 19-190 months) without any traced relapse. CONCLUSIONS: Total splenectomy is the treatment of choice of SH. Other surgical techniques could be employed in special cases.

[Ménétrier's disease and gastric cancer]. / Enfermedad de Ménétrier y cáncer gástrico.

Ménétrier's disease is an infrequent hypertrophic disease of the stomach associated with hypoproteinemia of unknown etiology. This disease is considered to be premalignant since 10-15% of affected individuals develop gastric cancer. We present a 66-year-old patient who had received a diagnosis of Ménétrier's disease 13 years previously and who was found to have advanced antral gastric cancer during follow-up. We provide an update on the optimal therapeutic approach, which has not been clearly defined to date.

Enfermedad de Ménétrier y cáncer gástrico / Ménétrier’s disease and gastric cancer

La enfermedad de Ménétrier es una gastropatía hipertrófica muy infrecuente, asociada a hipoproteinemia y de etiología desconocida. Es una condición preneoplásica, ya que se asocia a cáncer gástrico en un 10-15% de los casos. Presentamos a un paciente de 66 años diagnosticado de enfermedad de Ménétrier 13 años antes, que en el seguimiento presentó un cáncer gástrico antral avanzado. Se realiza una puesta al día del manejo terapéutico idóneo, ya que no está claramente definido (AU)

Ménétrier's disease is an infrequent hypertrophic disease of the stomach associated with hypoproteinemia of unknown etiology. This disease is considered to be premalignant since 10-15% of affected individuals develop gastric cancer. We present a 66-year-old patient who had received a diagnosis of Ménétrier's disease 13 years previously and who was found to have advanced antral gastric cancer during follow-up. We provide an update on the optimal therapeutic approach, which has not been clearly defined to date (AU)

[Primary small bowel lymphoma]. / Linfoma primario de intestino delgado.

We present four patients with non-Hodgkin's lymphoma of the small bowel. Three of the patients were men. Two patients presented with acute abdomen due to tumoral perforation and the remaining 2 presented with abdominal pain and other effects of the mass. The tumors were located in the ileum (1 patient), jejunum (2 patients) and jejunoileum (1 patient). All patients underwent resection of the affected segment. Three patients had large B-cell lymphomas and the remaining patient had a T-cell lymphoma associated with celiac disease. Different combinations of chemotherapy were administered. Only the patient with T-cell lymphoma died due to disease progression. Clinical aspects and the therapeutic strategy used in these tumors are discussed.

Linfoma primario de intestino delgado / Primary small bowel lymphoma

Presentamos a 4 pacientes afectados de linfoma no hodgkiniano de intestino delgado. Tres eran varones. En 2 pacientes se inició con un cuadro de abdomen agudo por perforación de la tumoración, y los otros 2 presentaban dolor abdominal y efecto masa. La tumoración se situaba en la zona del íleon (un caso), yeyuno (2 casos) y yeyunoileal (un caso). A todos ellos se efectuó resección del segmento intestinal afectado. En 3 casos se trataba de linfomas B de células grandes y el restante, un linfoma T asociado a celiaquía. Los pacientes han recibido diversas combinaciones de quimioterapia. Únicamente ha fallecido el paciente afectado de linfoma T por progresión de la enfermedad. Se debaten los aspectos clínicos y la estrategia terapéutica de estos tumores (AU)

We present four patients with non-Hodgkin's lymphoma of the small bowel. Three of the patients were men. Two patients presented with acute abdomen due to tumoral perforation and the remaining 2 presented with abdominal pain and other effects of the mass. The tumors were located in the ileum (1 patient), jejunum (2 patients) and jejunoileum (1 patient). All patients underwent resection of the affected segment. Three patients had large B-cell lymphomas and the remaining patient had a T-cell lymphoma associated with celiac disease. Different combinations of chemotherapy were administered. Only the patient with T-cell lymphoma died due to disease progression. Clinical aspects and the therapeutic strategy used in these tumors are discussed (AU)