ABSTRACT
Pigmented purpuric dermatoses are chronic vascular inflammatory conditions characterized by the presence of pigmented macules. Among its different presentations, lichen aureus is distinguished by the lichenoid conformation of its plaques and the predilection for lower limb involvement. Its segmented form is rare and difficult to control, especially in cases of symptomatic lesions. We report a rare case of segmental lichen aureus with six years of evolution associated with light itching. We also discuss the main therapeutic approaches to control the disease.
Subject(s)
Lichenoid Eruptions/pathology , Betamethasone/therapeutic use , Female , Glucocorticoids/therapeutic use , Humans , Lichenoid Eruptions/therapy , Methoxsalen/therapeutic use , Middle Aged , Photosensitizing Agents/therapeutic use , SunlightABSTRACT
Abstract: Pigmented purpuric dermatoses are chronic vascular inflammatory conditions characterized by the presence of pigmented macules. Among its different presentations, lichen aureus is distinguished by the lichenoid conformation of its plaques and the predilection for lower limb involvement. Its segmented form is rare and difficult to control, especially in cases of symptomatic lesions. We report a rare case of segmental lichen aureus with six years of evolution associated with light itching. We also discuss the main therapeutic approaches to control the disease.
Subject(s)
Humans , Female , Middle Aged , Lichenoid Eruptions/pathology , Sunlight , Betamethasone/therapeutic use , Photosensitizing Agents/therapeutic use , Lichenoid Eruptions/therapy , Glucocorticoids/therapeutic use , Methoxsalen/therapeutic useABSTRACT
The epidermal naevus syndrome (ENS) is a sporadic condition characterized by congenital epidermal naevi associated with anomalies in other organ systems, most commonly the central nervous system and skeleton. We report a case of ENS presenting hypophosphataemic rickets resistant to traditional therapeutic agents.
Subject(s)
Familial Hypophosphatemic Rickets/diagnosis , Nevus, Pigmented/diagnosis , Nevus, Sebaceous of Jadassohn/diagnosis , Skin Neoplasms/diagnosis , Child , Drug Resistance , Familial Hypophosphatemic Rickets/drug therapy , Familial Hypophosphatemic Rickets/physiopathology , Female , Follow-Up Studies , Humans , Nevus, Pigmented/physiopathology , Nevus, Sebaceous of Jadassohn/physiopathology , Skin Neoplasms/physiopathologyABSTRACT
Diffuse plane normolipemic xanthoma is a rare disease, of a group of clinical syndromes called histiocytoses, characterized by the presence of yellowish or yellow-orange plaques, distributed symmetrically on the cutaneous surface and usually accompanied by xanthelasma. It affects mainly adults and it may cause discrete changes in serum lipids. The case of an 85-year-old female patient who has been showing extensive asymptomatic yellow-orange plaques in the trunk and abdomen for a year is reported. Laboratory tests did not show an increase in serum lipids or the occurrence of reticuloendothelial disorders.
Subject(s)
Hypersplenism/complications , Xanthomatosis/complications , Xanthomatosis/pathology , Aged, 80 and over , Female , HumansABSTRACT
O xantoma plano difuso normolipêmico é doença rara, do grupo das histiocitoses, caracterizada pelo aparecimento de placas amareladas ou amarelo-alaranjadas, distribuídas simetricamente na pele e geralmente acompanhadas por xantelasma. Acomete principalmente adultos, podendo ou não apresentar alterações discretas dos lípides séricos. Relata-se o caso de uma paciente do sexo feminino, de 85 anos, há um ano com extensas placas amarelo-alaranjadas no tronco e abdome, assintomáticas. Os exames laboratoriais não demonstraram aumento dos lípides séricos, nem ocorrência de desordens retículo-endoteliais.
Diffuse plane normolipemic xanthoma is a rare disease, of a group of clinical syndromes called histiocytoses, characterized by the presence of yellowish or yellow-orange plaques, distributed symmetrically on the cutaneous surface and usually accompanied by xanthelasma. It affects mainly adults and it may cause discrete changes in serum lipids. The case of an 85-year-old female patient who has been showing extensive asymptomatic yellow-orange plaques in the trunk and abdomen for a year is reported. Laboratory tests did not show an increase in serum lipids or the occurrence of reticuloendothelial disorders.