ABSTRACT
El queratoquiste odontogénico constituye una entidad definida, con características histológicas y conducta biológica específica que permiten distinguirlos de otros quistesodontógenos productores de queratina. Se presentan en forma única o múltiple, la forma de presentación múltiple constituye uno de los criteriosmayores que obliga a la búsqueda deotras alteraciones asociadas que dan lugar a diferentes síndromes, siendo el más frecuente el Síndrome de Gorlin- Goltz´s. Se presentan tres casos de queratoquistes múltiples, describiendosus aspectos clínicos, radiográficos ehistopatológicos, realizando una breve revisión.
Subject(s)
Humans , Male , Female , Adolescent , Adult , Odontogenic Cysts/diagnosis , Odontogenic Cysts/etiology , Odontogenic Cysts , Basal Cell Nevus Syndrome/diagnosis , Basal Cell Nevus Syndrome/pathology , Basal Cell Nevus Syndrome , Argentina/epidemiology , Histological Techniques , Magnetic Resonance Imaging , Odontogenic Cysts/epidemiology , Data Interpretation, Statistical , Basal Cell Nevus Syndrome/epidemiology , Basal Cell Nevus Syndrome/ultrastructureSubject(s)
Basal Cell Nevus Syndrome/pathology , Carcinoma, Basal Cell/pathology , Adult , Aged , Basal Cell Nevus Syndrome/diagnosis , Basal Cell Nevus Syndrome/ultrastructure , Bone Diseases/pathology , Brain Diseases/pathology , Child , Humans , Jaw Cysts/pathology , Middle Aged , Skin Neoplasms/pathologySubject(s)
Basal Cell Nevus Syndrome/ultrastructure , Carcinoma, Basal Cell/ultrastructure , Jaw Cysts/ultrastructure , Adult , Basal Cell Nevus Syndrome/genetics , Epithelium/ultrastructure , Female , Humans , Jaw Cysts/genetics , Male , Mandibular Neoplasms/genetics , Mandibular Neoplasms/ultrastructure , Maxillary Neoplasms/genetics , Maxillary Neoplasms/ultrastructure , Microscopy, Electron , Middle AgedABSTRACT
Clinical, histopathological, electron-microscopical and cytophotometrical features of a case of linear unilateral basal cell nevus are reported. Several publications exist on basaliomas originating in a nevus verrucosus or nevus comedonicus. Our case, however, is regarded as an abortive form of the basal cell nevus syndrome due to somatic mutation. Only some few comparable cases are documented in the literature.