ABSTRACT
Valgus subtrochanteric osteotomies and hemiepiphyseodesis around the knees have been performed to correct severe coxa vara and genua valga in a girl patient who manifested extreme dwarfism associated with spondylometaepiphyseal dysplasia consistent with anauxetic dysplasia. To the best of our knowledge, this is the first description of the combined orthopaedic intervention in a girl with anauxetic dysplasia.
Subject(s)
Coxa Vara/surgery , Dwarfism/surgery , Femur/surgery , Genu Varum/surgery , Osteochondrodysplasias/surgery , Osteotomy , Tibia/surgery , Abnormalities, Multiple/genetics , Bone Plates , Casts, Surgical , Combined Modality Therapy , Coxa Vara/genetics , Disease Progression , Dwarfism/diagnostic imaging , Dwarfism/pathology , Epiphyses/surgery , Female , Genu Varum/congenital , Genu Varum/genetics , Humans , Osteochondrodysplasias/diagnostic imaging , Osteochondrodysplasias/pathology , Radiography , Restraint, PhysicalABSTRACT
We report the results of surgical treatment of congenital postero-medial bowing of the tibia and fibula. Twenty patients with congenital postero-medial bowing were seen with nine patients treated surgically (corrective osteotomy or lengthening and deformity correction with Ilizarov fixator) and 11 patients managed conservatively. The angles of medial and posterior angulation and limb length discrepancy were recorded serially and compared. Surgical complications were recorded. The mean follow-up was 9.5 and 6.1 years after surgery. Although there was a reduction in angulation and correction of limb length discrepancy, we encountered complications in the surgically treated patients. There was no statistically significant difference between the surgically treated and conservatively managed groups with respect to mean angulation, though there was a significant difference in the mean limb length discrepancy. In conclusion, we advocate a one-stage lengthening and correction of the residual deformity closer to skeletal maturity.
