Épulis congénito gigante: importancia del diagnóstico prenatal / Congenital giant cell epulis: Importance of the prenatal diagnosis

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Épulis congénito del recién nacido, una sorpresa para el Neonatólogo / Congenital epulis of the newborn, a surprise to the neonatologist

RESUMEN El épulis congénito del recién nacido es un tumor benigno, pediculado, de consistencia firme y tamaño variable, poco frecuente, de presentación bucal que tiene predilección por el sexo femenino. Se localiza habitualmente en la zona anterior y superior del maxilar superior. En caso de ser de gran tamaño puede interferir en la alimentación y dificultar la alimentación del neonato. La resección quirúrgica es el mejor tratamiento. El presente trabajo expone un caso y hace una revisión de la literatura.

ABSTRACT The congenital epulis of the newborn is a benign tumor, pedunculated, with a hard consistency and variable size rare, oral and of presentation that has a predilection for females. It is usually located in the anterior and superior maxilla. In case of big size it can interfere with feeding and can cause difficult neonatal feeding. Surgical resection is the best treatment. In this paper we presents a case and a review of the literature.

Prenatal diagnosis of congenital granular cell epulis.

Congenital granular epulis is a benign tumor that has rarely been diagnosed prenatally, although there have been numerous reports on its postnatal diagnosis. We report a case of large granular epulis diagnosed at 31 weeks' gestation in a woman whose previous anomaly scan had been normal. The lesion was 2.5 cm in diameter, pedunculated, and arose from the maxilla. It was completely surgically removed following preterm vaginal birth and histologically examined. The tumor did not prevent deglutition of the amniotic fluid and did not interfere with feeding or respiration, but prevented complete closure of the lips. We discuss the fetal management and the theories of histogenesis, and highlight the importance of early diagnosis and treatment.

[Granular cell congenital epulis: description of a case and literature review]. / Epulis congénital à cellules granuleuses: description d'un cas et revue de la littérature.

Case report of a voluminous gingival granular cell tumor (congenital epulis). Literature review concerning diagnosis, pathology, complications, evolution and treatment of this kind of tumor.

[Congenital epulis in the newborn]. / Epulis congénitale du nouveau-né.

The authors report a case of congenital epulis in the lower gum of a new born female. This rare benign tumor of the newborn is histologically characterized by the granular aspect of its cells. It occurs more frequently in females than in males. Differential diagnosis mainly concerns Abrikossoff tumor whose histogenesis and evolution are different. The distinctive features of epulis are the presence of a fusiform cell component and the negativity of the granular cells for PS100.

Congenital epulis.

A tumor was found to be arising from the right maxillary alveolar margin of a newborn baby. No other congenital abnormality was detected. Following excision and histopathological examination, diagnosis of benign congenital granular cell epulis was made. The post-operative course was uneventful.

[Congenital granular cell epulis].

Congenital granular cell epulis is an uncommon pedunculated tumor of the upper alveolar mucosa found only in newborns. The lesion is not usually associated with other congenital deformities, but presents a major esthetic problem and interferes with nursing. We present a case of a double epulis, 7 cm in diameter, in a 2-day-old girl. Treatment is simple excision, and no recurrences have been reported. The lesion must be differentiated from granular cell myoblastoma.

Congenital fibrous epulis: an undescribed fibrous lesion studied immunohistochemically and ultrastructurally.

Histological, immunohistochemical, and ultrastructural studies were done on a case of congenital gingival tumor with previously undescribed histopathological findings. The present lesion clinically mimicked a congenital epulis (congenital gingival granular cell tumor); however, it histologically consisted of densely packed collagen fibers forming numerous, well demarcated bundles surrounded by flattened cells with long slender cytoplasmic precesses. Immunohistochemical and ultrastructural findings suggested that these flattened cells embracing collagen bundles were fibroblastic in nature. Intracytoplasmic lysozomal granules could not be found in any cells of the lesion. Fibrous lesions similar to the present case have not been documented previously in the literature.

Multiple congenital epulides in a newborn: with special reference to reported cases in Japan.

This report describes a case of multiple epulides which simultaneously occurred on the maxilla and the mandible of a 6-day-old female baby. The clinical findings, diagnostic procedure, surgical treatment, histopathology, and 2-year follow-up of this case are presented. Based on the clinicostatistical and histopathologic investigations with special reference to the pertinent Japanese literature, a possible histogenetic etiology of this entity is discussed. Any odontogenic component might play an important role in the development of this tumor. This case of multiple epulides is considered to be very rare.

Congenital epulis in the newborn.

Neoplasms in the oral cavity are generally recognized during the routine examination of the newborn. Lesions arising on the alveolar processes of the jaws may interfere with nursing and respiration. This paper reviews the congenital epulis (CE) in the newborn. A case of CE arising on the maxillary alveolar process is reported. Due to the indication for removal of these benign tumours in the neonatal period they should be recognized as early as possible.

Congenital granular cell tumor of the tongue.

Granular cell lesions in the oral cavity occur primarily on the tongue in adults (granular cell tumor) and exclusively on the alveolar ridge in newborns (congenital granular cell epulis). Because of the location, age of appearance, and certain clinical and histologic differences, these histologically similar lesions are considered separate clinical entities. This case report, however, describes the occurrence of a granular cell lesion on the tongue of a newborn. Although the etiopathogenesis of these lesions is unknown, the present case suggests a common etiologic relationship of these entities and tends to rule out an odontogenic origin for the congenital granular cell epulis.

Congenital granular cell epulis causing polyhydramnios.

We report a case of an extremely large granular cell epulis situated on the maxillary alveolar ridge of a newborn. It obstructed the infant's mouth and caused polyhydramnios. The lesion was detected in utero by ultrasonography and removed after birth in the delivery room, with satisfactory results. It is evident that the epulis increased in size during the last phase of pregnancy. The literature concerning this peculiar lesion is reviewed and theories of histogenesis are discussed.