ABSTRACT
Biliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful surgical procedure. We highlight the importance of this unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery, regardless of age.
Subject(s)
Humans , Male , Female , Infant , Biliary Atresia/diagnosis , Late Onset Disorders/diagnosis , Liver/pathology , Biliary Atresia/pathology , Biliary Atresia/surgery , Biopsy , Diagnosis, Differential , Hepatic Artery/pathology , Late Onset Disorders/pathology , Late Onset Disorders/surgeryABSTRACT
Biliary atresia (BA) is classically described at the neonatal age. However, rare cases of BA in older infants have also been reported. We report four cases of late-onset BA in infants older than 4 weeks (3 males, 1 female), and describe the diagnostic and management difficulties. One of the cases had a late-onset (29 weeks) presentation with a successful surgical procedure. We highlight the importance of this unusual differential diagnosis in infants with cholestatic syndrome, who may benefit from Kasai surgery, regardless of age.