RESUMEN
Klippel-Feil syndrome (KFS) is a congenital anomaly characterized by a defect in the formation or segmentation of the cervical vertebrae, resulting in their fusion. The clinical triad of the syndrome consists of short neck, low posterior hairline, and limited neck movement, although fewer than 50 percent of patients demonstrate all three clinical features. The short neck and its immobility and instability present a significant challenge for endotracheal intubation. The purpose of this paper is to describe the management of a 13-year-old patient with KFS, extensive dental caries, and restricted mouth opening using a deep sedation technique in the operating room, which allowed successful completion of dental treatment.
Asunto(s)
Sedación Profunda/métodos , Caries Dental/rehabilitación , Caries Dental/terapia , Síndrome de Klippel-Feil/complicaciones , Adolescente , Manejo de la Vía Aérea , Anestesia General , Atención Dental para la Persona con Discapacidad , Asimetría Facial , Femenino , Humanos , Síndrome de Klippel-Feil/fisiopatología , Mandíbula/anomalías , Maxilar/anomalías , Tortícolis/complicacionesRESUMEN
Scurvy, vitamin C deficiency, is uncommon in industrialized societies today. Although supplementation of food with vitamin C has diminished its incidence, scurvy continues to occur in specific economically and nutritionally disadvantaged populations. The purpose of this report was to describe the case of infantile scurvy in a 20-month-old male with multisystem involvement including significant oral manifestations. Following an extensive initial evaluation, the multidisciplinary approach to diagnosis and management is discussed. This case demonstrates the need for heightened awareness of severe and multiplefood allergies in children and highlights disease conditions caused by nutritional deficiencies in this population.
