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Khirurgiia (Mosk) ; (1): 50-54, 2016.
Artículo en Ruso | MEDLINE | ID: mdl-26977611

RESUMEN

AIM: To evaluate the results of kidney transplantation from alive related donor in patients with Alport syndrome and to compare with those in patients with kidney hypoplasia. MATERIAL AND METHODS: We have analyzed 8 and 27 medical records of patients with Alport syndrome and kidney hypoplasia respectively. Following parameters were used - Kaplan-Meier survival analysis, Wilcox overall risk, percentage of transplants loss and mortality (Fisher's exact test calculation). RESULTS: It is concluded that percentage of transplants loss and mortality rate as well as overall survival and risk were similar in both groups. CONCLUSION: Despite risk of anti-GBM nephritis development in patients with Alport syndrome results are comparable with those after transplatation for chronic renal failure caused by other reasons.


Asunto(s)
Autoanticuerpos/inmunología , Fallo Renal Crónico/cirugía , Trasplante de Riñón , Riñón , Nefritis Hereditaria/cirugía , Nefritis , Adolescente , Adulto , Femenino , Humanos , Estimación de Kaplan-Meier , Riñón/patología , Riñón/cirugía , Trasplante de Riñón/efectos adversos , Trasplante de Riñón/métodos , Donadores Vivos , Masculino , Nefritis/diagnóstico , Nefritis/etiología , Nefritis/inmunología , Nefritis/mortalidad , Evaluación de Resultado en la Atención de Salud , Complicaciones Posoperatorias/diagnóstico , Complicaciones Posoperatorias/inmunología , Complicaciones Posoperatorias/mortalidad , Análisis de Supervivencia
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