Asunto(s)
Carcinoma Basocelular/secundario , Neoplasias Faciales/patología , Neoplasias Mandibulares/secundario , Neoplasias Nasales/patología , Cuero Cabelludo/patología , Neoplasias Cutáneas/patología , Anciano de 80 o más Años , Carcinoma Basocelular/cirugía , Neoplasias Faciales/cirugía , Femenino , Humanos , Metástasis Linfática , Masculino , Neoplasias Mandibulares/cirugía , Neoplasias Nasales/cirugía , Neoplasias Cutáneas/cirugíaRESUMEN
The purpose of this article was to report a pediatric case of secondary cervical esthesioneuroblastoma involving the parapharyngeal lymph nodes. A 3-year-old boy came to our clinical observation because of a right lymphonodal mass evidenced by nuclear magnetic resonance and a diagnosis of Cushing syndrome associated with ectopic adrenocorticotropic hormone secretion, moon face, central obesity, asthenia, and hirsutism. At the age of 10 months, the patient underwent endoscopic surgery for asportation of the World Health Organization stage IV esthesioneuroblastoma. At 38 months of age, the patient underwent right parapharyngeal lymphadenectomy with surgical access by a double mandibulectomy. After surgery, serum ACTH, cortisolemia, and urinary excretion of cortisol were within the reference range. Blood pressure was recorded at 110/70 mm Hg. Moon face disappeared, as well as central obesity and hirsutism. Clinical report is presented together with brief review of literature.