Central mucoepidermoid carcinoma--a case report.

The mucoepidermoid carcinoma (MEC) account for approximately 6-8 Percent of all salivary gland tumors. Central mucoepidermoid carcinoma of the jaws is rare. Following is a case report of central mucoepidermoid carcinoma which involves the ramus of the mandible. Origin of the central mucoepidermoid carcinoma is discussed.

Apert syndrome: a case report with discussion of craniofacial features.

Apert syndrome is a rare congenital anomaly characterized by acrocephaly, syndactyly, and abnormalities of other organs. It has characteristic features in the orofacial region, affecting the eyes, palate, middle third of face, and uvula. In this case report, the features of Apert syndrome, particularly in relation to the orofacial region, are discussed.

Maxillary metastasis of osteosarcoma.

Osteosarcoma, either primary or metastatic, rarely involves the jaws. Though only a few cases of mandibular metastasis of osteosarcoma have been reported, only one case of et al maxillary involvement (Singh, 1978) has been reported. A case of 21 year old boy with metastasis of osteosarcoma to the right maxilla from primary osteosarcoma of the left femur is presented. The patient complained of pain and swelling in the left maxillary region which was earlier diagnosed as maxillary sinusitis on the basis of Water's sinus radiograph in a medical hospital. Further radiographic examination with the panoramic and intraoral periapical radiographs done by us and later by fine needle aspiration cytology led us to diagnose a secondary deposits of osteosarcoma.

Primary intraosseous carcinoma of the jaws originating in odontogenic cysts.

Primary intraosseous carcinoma (PIOC) of the jaws is a rare lesion and majority of them arise from the epithelial lining of pre-existing odontogenic cysts (OCS). In a case of 20 year old male, PIOC presented a painless swelling extending from left posterior side of the mandible to across the midline with a duration of three months. X-rays revealed a cystic Unilocular radiolucency with well demarcated margin. Aspiration revealed the characteristics of cystic fluid. Histological examination of the biopsy specimen following marsupialisation showed SCA arising in cystic lining. In another case of 24 year old female, PIOC presented a painless swelling on the right side of the mandible with a hollow cavity seen intraorally in the region of the first molar, exfoliated itself in one month. X-rays revealed a cystic radiolucency but with irregular margin centrally. Histologic examination of a biopsy specimen from the lining of the cavity showed SCA originating in cystic lining. In both cases habit of tobacco was absent.

Metastatic malignant melanoma of maxillary gingiva. A case report.

Malignant melanoma of the oral cavity can be primary or secondary due to metastasis from distant site. Incidence of oral cavity by metastasis of melanoma is 1.85%. Most common oral sites involved are tongue, buccal mucosa and parotid gland. Oral lesions occur as a part of disseminated disease during the advanced stages and has poor prognosis. An unusual case of metastatic malignant melanoma of the maxillary gingiva is reported.

Hyalinosis cutis et mucosae. Review with a case report.

Hyalinosis cutis et mucosae (lipoid proteinosis) is a rare disorder characterized by hyaline and lipid deposits in the skin and mucous membrane of the oral cavity, upper respiratory tract, and internal organs. It usually appears in infancy with hoarseness. This disorder is particularly interesting because of its rarity and wide range of clinical manifestations. We report a case that demonstrated manifestations of lipoid proteinosis.

Aglossia: a case report.

The case of a 30-year-old man with aglossia is reported. Aglossia, a rare condition, is a developmental disorder in which the entire tongue is absent. It is usually associated with jaw and facial anomalies. In this patient, both the maxilla and mandible were affected. Although the mortality rate of patients with aglossia is high, this patient has been able to cope with his oral function with minimal obstruction.

Oro-facial granulomatosis. A review of literature with report of five cases.

Five cases of oro-facial granulomatosis are reported. The literature pertaining to this and related lesions is reviewed with respect to diagnosis, histology and management of the lesions.

Cheilitis glandularis.

Cheilitis glandularis is reported in two farmers with characteristic clinical and histopathological features. Both patients were treated with vermilionectomy. The prognosis was good.

Orofacial manifestations of Sturge-Weber syndrome. Review with a case report.

Sturge-Weber syndrome is reported in a 19 year old male. Intraoral manifestations of SWS are uncommon. Hence, the present case is reported for the presence of gingival capillary hemangioma which was surgically treated. A review from the literature pertaining to orofacial manifestations of SWS is given.

Usefulness of serum glycoconjugates in precancerous and cancerous diseases of the oral cavity.

Sera from 47 healthy controls, 18 normal individuals with the habit of tobacco chewing, 43 patients with oral precancerous (PC) conditions, and 40 patients with oral cancer (OC) were studied for the levels of total sialic acid (TSA), lipid-bound sialic acid (LSA), mucoid proteins, and protein-bound hexoses (PBH) (galactose and mannose). The changes in the glycoconjugate levels were insignificant between the controls and the normal tobacco chewers. All four parameters were significantly elevated in oral PC patients compared with controls. The levels of PBH and LSA showed significant increase in the oral PC patients compared with the normal tobacco chewers. A significant increase was observed in the levels of TSA, LSA, mucoid proteins, and PBH in OC patients compared with controls, normal tobacco chewers, and patients with oral PC. Increasing levels of all the biomarkers were found with progression of the malignant disease. Elevations in the levels of TSA and LSA were statistically significant in Stage IV patients compared with Stage III patients. The patients with metastases had higher levels of the biomarkers than the patients with primary OC. However, elevations only in LSA levels were statistically significant. These results suggest that evaluations of the serum glycoconjugate levels may be useful in diagnosis of the patients with oral PC or OC. In addition to their value in early detection, they can also help in staging of the disease.

Aarskog syndrome. A case report.

A rare Aarskog syndrome is reported in a 12-year-old boy. The patient had a triad of characteristic symptoms consisting of short stature, genital anomaly, and unusual facies. Both jaws were hypoplastic with presence of crowded permanent teeth and over-retained deciduous teeth. Radiographic examination of teeth showed taurodontism, which has not been reported previously.

Orofacial manifestations of myofascial pain dysfunction syndrome amongst dental patients.

Orofacial manifestations in cases of Myofascial Pain Dysfunction Syndrome (MPD) diagnosed amongst 71 Dental patients were studied in detail. Findings of this study show that the chief complaint and associated orofacial manifestations of MPD are related to muscular hypertonicity. Stressful situations may produce muscular hypertension, which leads to muscle tenderness as a symptom of over work and fatigue. MPD may be considered a psycosomatic disease.