RESUMEN
Leiomyomatosis peritonealis disseminata is an uncommon condition characterized by subperitoneal proliferation of benign nodules mainly composed of benign smooth muscle cells. This entity generally appears in premenopausal women and hormonal influences may play a role in its pathogenesis. The macroscopic appearance mimics peritoneal carcinomatosis. The characteristic clinical course is asymptomatic and diagnosis is only feasible after microscopic examination. To date, less than 100 cases have been reported in the literature. We report the case of a 40-year-old woman who underwent surgery in our department.
Asunto(s)
Leiomiomatosis/diagnóstico por imagen , Leiomiomatosis/patología , Neoplasias de Tejido Conjuntivo/diagnóstico por imagen , Neoplasias de Tejido Conjuntivo/patología , Adulto , Femenino , Humanos , Leiomiomatosis/cirugía , Imagen por Resonancia Magnética , Músculo Liso/patología , Músculo Liso/cirugía , Neoplasias de Tejido Conjuntivo/cirugía , Peritoneo/diagnóstico por imagen , Peritoneo/patología , Peritoneo/cirugía , Tomografía Computarizada por Rayos XRESUMEN
La leiomiomatosis peritoneal diseminada es una entidad rara que se caracteriza por la proliferación subendotelial de nódulos básicamente compuestos de células de músculo liso. Aparece de forma general en mujeres premenopáusicas y su patogenia tiene gran influencia hormonal. Simula macroscópicamente una carcinomatosis peritoneal. De forma característica cursa de forma indolente y el diagnóstico es sólo posible tras el examen histológico. Se han descrito menos de 100 casos en la literatura científica hasta la fecha. Presentamos un caso de una paciente de 40 años intervenida en nuestro servicio (AU)
Leiomyomatosis peritonealis disseminata is an uncommon condition characterized by subperitoneal proliferation of benign nodules mainly composed of benign smooth muscle cells. This entity generally appears in premenopausal women and hormonal influences may play a role in its pathogenesis. The macroscopic appearance mimics peritoneal carcinomatosis. The characteristic clinical course is asymptomatic and diagnosis is only feasible after microscopic examination. To date, less than 100 cases have been reported in the literature. We report the case of a 40-year-old woman who underwent surgery in our department (AU)