RESUMEN
INTRODUCTION: Retroperitoneal liposarcomas are rare malignant tumors known for their slow growth and challenging management, particularly due to their substantial size upon diagnosis. This case report highlights a remarkable instance of a massive retroperitoneal sarcoma concomitant with synchronous renal cell carcinoma. CASE PRESENTATION: We report a 57-year-old male patient with a huge abdominal mass hampering his daily activities and on further investigation, CECT abdomen and pelvis revealed a large Retroperitoneal Scarcoma (RPS) occupying his entire abdominal cavity displacing the visceral organs. In accordance with the final decision of the multi-disciplinary team meeting, he was subjected for surgery and the tumor was excised enbloc. He is kept under surveillance. DISCUSSION: Surgery remains the main modality of treatment for RPS. Hence careful preoperative surgical planning and execution with meticulous dissection aids in achieving a good clinical outcome and to reduce recurrence in future. CONCLUSION: Despite the huge size of the tumor, surgical intervention remains the primary treatment option whenever feasible, often complemented by additional therapeutic approaches.
RESUMEN
Terminal myelocystoceles (TMCs) are a rare form of occult spinal dysraphism. They constitute approximately 5% of skin covered lumbosacral masses. The TMC is composed of a low-lying conus medullaris with cystic dilatation of caudal central canal, a surrounding meningocele and a lipoma that extends from the conus to a subcutaneous fat collection. A 6-month-old female child presented with a large lumbosacral mass (14 cm × 12 cm × 10 cm) and weakness at the ankle joints since birth. Magnetic resonance imaging and computed tomography scan revealed a low-lying terminal lipomyelocystocele with holocord syrinx and partial sacral agenesis. The child was operated on successfully. This is an interesting and rare case of giant terminal lipomyelocystocoele with syrinx and a partial sacral agenesis. Terminal lipomyelocystocele should be included in the differential diagnosis of congenital lesions presenting as a lumbosacral mass and operated early.
