RESUMEN
El hemangioendotelioma epitelioide es un tumor vascular infrecuente, descrito por primera vez en 1975 por Dail y Liebow como un carcinoma bronquioloalveolar. Habitualmente, se comporta como una neoplasia de bajo grado; sin embargo, se han descrito casos en los que el tumor manifiesta una elevada agresividad, extendiéndose con rapidez por todo el organismo. Presentamos el caso de un hombre de 41 años con dermatosis en muslo izquierdo y extensión rápida a abdomen, cuyo diagnóstico inicial fue de un carcinoma metastásico vs. linfoma. En la revisión de laminillas, se confirmó el diagnóstico de hemangioendotelioma epitelioide de piel, iniciando tratamiento con radioterapia. Este tumor afecta excepcionalmente la piel, habiéndose descrito pocos casos en la literatura médica.(AU)
Epithelioid haemangioendothelioma is a rare vascular tumor, first described in 1975 by Dail and Liebow as a bronchioloalveolar carcinoma. Although it usually behaves like a low-grade neoplasm, cases have been reported in which the tumor shows a high grade of malignancy, spreading rapidly throughout the body. We present the case of a 41-year-old man with dermatosis in the left thigh with rapid extension to the abdomen; the initial differential diagnoses were metastatic carcinoma versus lymphoma. When the histopathology was re-examined, a diagnosis of skin epithelioid hemangioendothelioma was confirmed and treatment with radiotherapy was initiated. This tumour rarely affects the skin; there are only a few previously reported cases.(AU)
Asunto(s)
Humanos , Masculino , Adulto , Hemangioendotelioma Epitelioide/diagnóstico , Neoplasias Cutáneas , Neoplasias de Tejido Vascular , Pacientes Internos , Examen Físico , Evaluación de Síntomas , Resultado del Tratamiento , Dermatosis de la Pierna , Patología , Servicio de Patología en Hospital , NeoplasiasRESUMEN
Epithelioid haemangioendothelioma is a rare vascular tumor, first described in 1975 by Dail and Liebow as a bronchioloalveolar carcinoma. Although it usually behaves like a low-grade neoplasm, cases have been reported in which the tumor shows a high grade of malignancy, spreading rapidly throughout the body. We present the case of a 41-year-old man with dermatosis in the left thigh with rapid extension to the abdomen; the initial differential diagnoses were metastatic carcinoma versus lymphoma. When the histopathology was re-examined, a diagnosis of skin epithelioid hemangioendothelioma was confirmed and treatment with radiotherapy was initiated. This tumour rarely affects the skin; there are only a few previously reported cases.