Peripheral odontogenic fibroma in a child with Ellis-van Creveld syndrome: Case report.

INTRODUCTION: Ellis-van Creveld (EVC) syndrome is an autosomal recessive disorder predominantly characterized by a disproportionate dwarfism, ectodermal dysplasia, postaxial polydactyly, and congenital heart malformations and pulmonary hypoplasia. OBJECTIVE: In this article, we hereby present a case of a 6-year-old Brazilian boy with EVC syndrome who presented a rare oral lesion as well as a remarkable number of classical and uncommon oral and dental features. CASE REPORT: Clinical and radiographic examination revealed multiple enamel hypoplasia, teeth agenesis, conical teeth, lower canine rotation, bilateral posterior crossbite, taurodontism of deciduous and permanent molars and delayed tooth eruption, dental caries, and absent vestibular sulcus. Additionally, a whitish lobulated nodule located in the alveolar ridge in the anterior region of the mandible was noted. Anatomopathological examination was compatible with the diagnosis of peripheral odontogenic fibroma (POF). In a 10-month clinical follow-up, no signs of recurrence were observed. CONCLUSION: In view of the characteristic oral findings of EVC syndrome and the potential for recurrence of POF, the pediatric dentist plays an essential role in clinical follow-up, planning and preventive, and rehabilitative treatment.

Técnica de micromarsupialización en ránula oral: reporte de dos casos clínicos en paciente infantil / Técnica de micromarsupialização em rânula oral: relato de dois casos clínicos em paciente infantil / Micromarsupialization technique in oral ranula: report of two clinical cases in child patient

Introducción: Ránulas orales son pseudoquistes resultantes de la retención de mucus o extravasación de saliva que suelen afectar a los niños. Este artículo tiene como objetivo reportar dos casos clínicos de ránulas orales y discutir el tratamiento mediante la técnica de micromarsupialización. Reporte de caso 1: Niña de 6 años de edad, acudió al servicio de urgencia en odontopediatría de la Bebé Clínica de la Universidad Estatal de Londrina refiriendo "bolita debajo de la lengua" de aproximadamente 3 meses de evolución. Clínicamente se observó burbuja rojiza de aproximadamente 1,5 cm de diámetro ubicada en el lado derecho del suelo bucal en forma de cúpula, base sésil y fluctuante. Reporte de caso 2: Niña de 5 años, acudió al mismo servicio con queja de "burbuja en la lengua" de aproximadamente 2 meses de evolución. Clínicamente se observó burbuja de color rosado similar a la mucosa de aproximadamente 1 cm de diámetro ubicada en el lado izquierdo del suelo bucal con forma circunscrita, base sésil y fluctuante. Con base en los aspectos clínicos y la historia actual de las lesiones, el diagnóstico fue ránula oral y el tratamiento quirúrgico realizado fue micromarsupialización. En el seguimiento clínico de 8 y 6 meses, respectivamente, hubo regresión total de las lesiones sin signos clínicos de recurrencia. Conclusión: Con base en dos casos clínicos reportados, se puede concluir que el uso de la técnica de micromarsupialización representa procedimiento quirúrgico efectivo en niños por su rápida ejecución, abordaje conservador, sin el uso de anestesia local infiltrativa, bien tolerado y con buen pronóstico.

Introdução: Rânulas orais são pseudocistos resultantes da retenção de muco ou extravasamento de saliva que frequentemente acometem crianças. Este artigo objetiva relatar dois casos clínicos de rânulas orais e discutir o tratamento utilizando a técnica de micromarsupialização. Relato de caso 1: menina de 6 anos, compareceu ao Pronto-Socorro da Bebê Clínica da Universidade Estadual de Londrina queixando-se de "bola embaixo da língua" com duração aproximada de 3 meses. Ao exame intraoral, notou-se bolha avermelhada de aproximadamente 1,5 cm de diâmetro localizada no lado direito do assoalho bucal em forma de cúpula, base séssil e flutuante. Relato de caso 2: menina de 5 anos, compareceu ao mesmo serviço com queixa de "bolha na língua" com duração aproximada de 2 meses. Clinicamente, notou-se bolha de coloração rósea igual à mucosa de aproximadamente 1 cm de diâmetro localizada no lado esquerdo do assoalho bucal de formato circunscrito, base séssil e flutuante. Com base nos aspectos clínicos e na história atual das lesões, o diagnóstico foi de rânula oral e o tratamento cirúrgico realizado foi a micromarsupialização. Em acompanhamento clínico de 8 e 6 meses, respectivamente, foi observado regressão total das lesões sem sinais clínicos de recidiva. Conclusão: A partir dos casos clínicos relatados, pode-se concluir que a utilização da técnica de micromarsupialização representa um procedimento cirúrgico eficaz em crianças devido à rápida execução, abordagem conservadora, sem uso de anestesia local infiltrativa, bem tolerada e com bom prognóstico.

Introduction: Oral ranulas are pseudocysts resulting from the retention of mucus or extravasation of saliva that often affect children. This article aims to report two clinical cases of oral ranulas and discuss the treatment using the micromarsupialization technique. Case report 1: 6-year-old girl, attended the Emergency Room of the Baby Clinic of the State University of Londrina complaining of a "ball under the tongue" lasting approximately 3 months. Clinically, reddish bubble of approximately 1.5 cm in diameter was noted located on the right side of the dome-shaped mouth floor, sessile base and fluctuating. Case report 2: 5-year-old girl, attended the same service with a complaint of "bubble on the tongue" lasting approximately 2 months. Clinically, pink-colored bubble similar to the mucosa of approximately 1 cm in diameter was observed located on the left side of the floor of the mouth with a circumscribed shape, sessile base and fluctuating. Based on the clinical aspects and the current history of the lesions, the diagnosis was oral ranula and the surgical treatment performed was micromarsupialization. In a clinical follow-up of 8 and 6 months, respectively, total regression of the lesions was observed, with no clinical signs of recurrence. Conclusion: Based on the reported clinical cases, it can be concluded that the use of micromarsupialization technique represents an effective surgical procedure in children due to its quick execution, conservative approach, without the use of local infiltrative anesthesia, well tolerated and with good prognosis.

Manifestaciones orales en paciente infantil con síndrome de Ellis-van Creveld: informe de caso / Manifestações orais em paciente infantil com síndrome de Ellis-van Creveld: relato de caso / Oral manifestations in child patient with Ellis-van Creveld syndrome: case report

El síndrome de Ellis-van Creveld es un trastorno autosómico recesivo caracterizado por una tétrada de enanismo desproporcionado, displasia ectodérmica, polidactilia postaxial y malformaciones cardíacas congénitas. En este artículo, presentamos el caso de un niño brasileño de 6 años con síndrome de Ellis-van Creveld que presentó un número notable de características orales y dentales clásicas y hallazgos poco comunes como taurodontismo. El examen clínico reveló hipoplasia múltiple del esmalte, surco vestibular ausente, aserraduras alveolares en la región anterior del maxilar, dientes ausentes, dientes cónicos, canino inferior girado, mordida cruzada posterior bilateral, caries dental y un nódulo. Radiográficamente se observa agenesia dentaria, taurodontismo de molares primarios y permanentes y retraso en la erupción dentaria. Los hallazgos clínicos y radiográficos pueden estar presentes desde el nacimiento y el odontopediatra tiene un papel fundamental en el diagnóstico precoz del síndrome de Ellis-van Creveld, así como en la prevención de problemas orales, rehabilitación e intervenciones estéticas.

A síndrome de Ellis-van Creveld é uma doença autossômica recessiva caracterizada por uma tétrade de baixa estatura desproporcional, displasia ectodérmica, polidactilia pós-axial e malformações cardíacas congênitas. Neste artigo, será relatado um caso de um menino brasileiro de 6 anos de idade com síndrome de Ellis-van Creveld que apresenta um número notável de características orais e dentárias clássicas e achados incomuns como taurodontismo. Ao exame clínico foi revelado hipoplasia múltipla do esmalte, sulco vestibular ausente, serrilhas alveolares na maxila anterior, dentes ausentes, dentes cônicos, canino inferior rotacionado, mordida cruzada posterior bilateral, cárie dentária e um nódulo. Radiograficamente, foi observado agenesia dentária, taurodontismo de molares decíduos e permanentes e atraso na erupção dentária. Os achados clínicos e radiográficos podem estar presentes desde o nascimento e o odontopediatra tem papel fundamental no diagnóstico precoce da síndrome de Ellis-van Creveld, bem como na prevenção de problemas bucais, reabilitação e intervenções estéticas.

Ellis­van Creveld syndrome is an autosomal recessive disorder characterized by a tetrad of disproportionate dwarfism, ectodermal dysplasia, postaxial polydactyly, and congenital heart malformations. In this article, we hereby present a case of a 6-year-old Brazilian boy with Ellis­van Creveld syndrome who presented with a remarkable number of classical oral and dental features and uncommon findings such as taurodontism. Clinical examination revealed multiple enamel hypoplasia, absent vestibular sulcus, alveolar serrations in the maxilla anterior region, missing teeth, conical teeth, lower canine rotation, bilateral posterior crossbite, dental caries, and a nodule. Radiographically were observed teeth agenesis, taurodontism of deciduous and permanent molars, and delayed tooth eruption. Clinical and radiographic findings may be present from birth and the pediatric dentist has a fundamental role in the early diagnosis of Ellis­van Creveld syndrome, as well as oral problems prevention, rehabilitation, and aesthetic interventions.

Different dimensions of oral health literacy are associated with social determinants of health in Brazilian adults.

Social determinants of health (SDH) are strongly associated with oral health outcomes, and oral health literacy (OHL) is a potential factor that can modify this association. This study evaluated the association between SDH and OHL, including functional and interactive dimensions of OHL. The cross sectional study was conducted with 354 adults recruited from public dental clinics in southern Brazil. Functional OHL was measured using the Brazilian version of the Rapid Estimate of Adult Literacy in Dentistry (BREALD-30) and the Health Literacy Dental Scale (HeLD-14), for the evaluation of interactional OHL. SDH was evaluated through a structured questionnaire, and economic class was determined based on the Brazilian Economic Classification Criteria. The statistical analysis involved bivariate and multivariate Poisson regression with robust variance (α=0.05) to estimate rate ratios (RR) and 95% confidence intervals (CI). Among the 354 participants, 284 (80.2%) were women and the mean age was 22.9 ± 4.9 years. The median BREALD-30 score was 24 (1st/3rd quintile: 20/27) and the median HeLD-14 score was 45 (1st/3rd quintile: 37/50). Most participants had up to eight years of schooling (71.5%) and belonged to the "C" Economic Class or lower (94.1%). The multiple regression analysis showed that schooling and economic class were associated with the BREALD-30 and HeLD-14 scores, income and age were associated with the HeLD-14 score, and marital status and occupation were associated with the BREALD-30 score. Different dimensions of OHL were associated with SDH in Brazilian adults. This aspect should be incorporated into strategies for improving OHL levels in individuals or populations.

Different dimensions of oral health literacy are associated with social determinants of health in Brazilian adults

Abstract Social determinants of health (SDH) are strongly associated with oral health outcomes, and oral health literacy (OHL) is a potential factor that can modify this association. This study evaluated the association between SDH and OHL, including functional and interactive dimensions of OHL. The cross sectional study was conducted with 354 adults recruited from public dental clinics in southern Brazil. Functional OHL was measured using the Brazilian version of the Rapid Estimate of Adult Literacy in Dentistry (BREALD-30) and the Health Literacy Dental Scale (HeLD-14), for the evaluation of interactional OHL. SDH was evaluated through a structured questionnaire, and economic class was determined based on the Brazilian Economic Classification Criteria. The statistical analysis involved bivariate and multivariate Poisson regression with robust variance (α=0.05) to estimate rate ratios (RR) and 95% confidence intervals (CI). Among the 354 participants, 284 (80.2%) were women and the mean age was 22.9 ± 4.9 years. The median BREALD-30 score was 24 (1st/3rd quintile: 20/27) and the median HeLD-14 score was 45 (1st/3rd quintile: 37/50). Most participants had up to eight years of schooling (71.5%) and belonged to the "C" Economic Class or lower (94.1%). The multiple regression analysis showed that schooling and economic class were associated with the BREALD-30 and HeLD-14 scores, income and age were associated with the HeLD-14 score, and marital status and occupation were associated with the BREALD-30 score. Different dimensions of OHL were associated with SDH in Brazilian adults. This aspect should be incorporated into strategies for improving OHL levels in individuals or populations.