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1.
Lupus ; : 9612033241281610, 2024 Sep 17.
Artículo en Inglés | MEDLINE | ID: mdl-39285729

RESUMEN

Two cases of chilblain lupus erythematosus (CLE) potentially triggered by exposure to ultraviolet (UV) nail lamps are presented. These cases, along with a review of the literature, suggest a possible link between UV nail lamp use and CLE development or reactivation. Further research is needed to confirm this association, but healthcare professionals should be aware of the potential risks of this practice, especially for patients with photosensitive conditions.

2.
Pediatr Dermatol ; 41(1): 96-99, 2024.
Artículo en Inglés | MEDLINE | ID: mdl-37515487

RESUMEN

Serine/threonine kinase 4 deficiency (STK4 or MST1, OMIM:614868) is an autosomal recessive (AR) combined immunodeficiency that can present with skin lesions such as epidermodysplasia verruciformis-like lesions (EVLL). Herein, we describe a 17-year-old male patient born from consanguineous parents presenting with recurrent respiratory infections, verruciform plaques, poikiloderma, chronic benign lymphoproliferation, and Sjögren syndrome with suspected interstitial lymphocytic pneumonia.


Asunto(s)
Epidermodisplasia Verruciforme , Enfermedades de Inmunodeficiencia Primaria , Enfermedades de la Piel , Masculino , Humanos , Adolescente , Epidermodisplasia Verruciforme/diagnóstico , Epidermodisplasia Verruciforme/genética , Epidermodisplasia Verruciforme/patología , Papillomaviridae , Enfermedades de Inmunodeficiencia Primaria/diagnóstico , Proteínas Serina-Treonina Quinasas , Péptidos y Proteínas de Señalización Intracelular
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