Desmoplastic fibroma in a child: a 9-year follow-up case report.

BACKGROUND: Desmoplastic fibroma is an extremely rare primary bone tumor. Its characteristic features include bone destruction accompanied by the formation of soft tissue masses. This condition predominantly affects individuals under the age of 30. Since its histology is similar to desmoid-type fibromatosis, an accurate diagnosis before operation is difficult. Desmoplastic fibroma is resistant to chemotherapy, and the efficacy of radiotherapy is uncertain. Surgical excision is preferred for treatment, but it entails high recurrence. Further, skeletal reconstruction post-surgery is challenging, especially in pediatric cases. CASE PRESENTATION: Nine years ago, a 14-year-old male patient presented with a 4-year history of progressive pain in his left wrist. Initially diagnosed as fibrous dysplasia by needle biopsy, the patient underwent tumor resection followed by free vascularized fibular proximal epiphyseal transfer for wrist reconstruction. However, a histological examination confirmed a diagnosis of desmoplastic fibroma. The patient achieved bone union and experienced a recurrence in the ipsilateral ulna 5 years later, accompanied by a wrist deformity. He underwent a second tumor resection and wrist arthrodesis in a single stage. The most recent annual follow-up was in September 2023; the patient had no recurrence and was satisfied with the surgery. CONCLUSIONS: Desmoplastic fibroma is difficult to diagnose and treat, and reconstruction surgery after tumor resection is challenging. Close follow-up by experienced surgeons may be beneficial for prognosis.

Theoretical and experimental investigation on decomposition mechanism of eco-friendly insulation gas HFO1234zeE.

Decomposition experiments under corona discharge and theoretical calculations using the density functional theory (DFT) method were accomplished to clarify the dissociation behavior and decomposition mechanism of HFO1234zeE (trans-1,3,3,3-tetrafluoropropene), an eco-efficient SF6 alternative gas. The discharge decomposition products of HFO are mainly fluorocarbon, unsaturated hydrocarbon and saturated hydrocarbons, which are containing no more than three carbons. Free radicals, CF3·, F· and H·, generated via bond-cleavage reaction are important structures to promote the decomposition, and HFO is more likely to dissociate with them by abstraction reaction to form CF4 and CF3H. Long-chain radicals, such as CF3CHCF·, CF3CHCH· and CF3CCHF·, will be decomposed into CF3CCH and CF3CCF, and small intermediates would be easier to combine to form HF, C2F6, C2F4, C2HF5, CF3HCF3H and C3F8. It is also likely to be converted to Z-isomer. Due to the high discharge intensity and ion bombardment, solid by-products appeared on the electrode surface may contain carbon dust and metal compounds. The solid attached to the surface has little effect on the electric field distribution, and most gas decomposition products still maintain the insulation strength, so the air-gap breakdown voltage only dropped by about 6.2% after long-term corona discharge. The obtained results not only reveal the decomposition mechanism in a comprehensive way, but also present useful reference for exploring the application potentials of HFO1234zeE.