RESUMEN
Bart's syndrome is characterized by three clinical manifestations: epidermolysis bullosa, congenital absence of skin, and nail abnormalities. It is believed that congenital skin absence follows the patterns of Blaschko's lines. Treatment seeks to prevent secondary infection. Prognosis is favorable and depends upon the healing of lesions.
Asunto(s)
Epidermólisis Ampollosa , Uñas Malformadas , Anomalías Cutáneas , Epidermólisis Ampollosa/patología , Femenino , Humanos , Recién Nacido , Uñas Malformadas/patología , Anomalías Cutáneas/patología , SíndromeRESUMEN
A síndrome de Bart é caracterizada pela tríade de manifestações clínicas: epidermólise bolhosa, aplasia de cútis e anormalidades ungueais. Presume-se que a ausência congênita de pele segue as linhas de Blaschko. O tratamento visa a evitar infecções secundárias. O prognóstico é bom e depende da cicatrização das bolhas.
Bart's syndrome is characterized by three clinical manifestations: epidermolysis bullosa, congenital absence of skin, and nail abnormalities. It is believed that congenital skin absence follows the patterns of Blaschko's lines. Treatment seeks to prevent secondary infection. Prognosis is favorable and depends upon the healing of lesions.
Asunto(s)
Femenino , Humanos , Recién Nacido , Epidermólisis Ampollosa , Uñas Malformadas , Anomalías Cutáneas , Epidermólisis Ampollosa/patología , Uñas Malformadas/patología , Síndrome , Anomalías Cutáneas/patologíaRESUMEN
We report the case of a rare anomaly of the right coronary artery (RCA) arising from the left aortic sinus, having a single ostium with the left coronary artery, associated with documented episodes of inferior ischemia, in which surgical treatment with a right internal thoracic artery to RCA bypass graft and the corresponding ligation provided greater stability to the coronary blood flow and good clinical progress.
Asunto(s)
Anomalías de los Vasos Coronarios , Seno Aórtico/anomalías , Cineangiografía , Angiografía Coronaria , Puente de Arteria Coronaria , Anomalías de los Vasos Coronarios/diagnóstico por imagen , Anomalías de los Vasos Coronarios/cirugía , Humanos , Masculino , Persona de Mediana Edad , Seno Aórtico/diagnóstico por imagenRESUMEN
Relatamos caso de rara anomalia de coronária direita (CD) originando em seio aórtico esquerdo, óstio único com coronária esquerda, associado a episódios de isquemia inferior documentados, no qual o tratamento cirúrgico com "by pass" de artéria torácica interna direita para CD com respectiva ligadura proporcionou maior estabilidade ao fluxo coronário, com boa evolução clínica.
We report the case of a rare anomaly of the right coronary artery (RCA) arising from the left aortic sinus, having a single ostium with the left coronary artery, associated with documented episodes of inferior ischemia, in which surgical treatment with a right internal thoracic artery to RCA bypass graft and the corresponding ligation provided greater stability to the coronary blood flow and good clinical progress.
Asunto(s)
Humanos , Masculino , Persona de Mediana Edad , Anomalías de los Vasos Coronarios , Seno Aórtico/anomalías , Cineangiografía , Angiografía Coronaria , Puente de Arteria Coronaria , Anomalías de los Vasos Coronarios , Anomalías de los Vasos Coronarios/cirugía , Seno AórticoRESUMEN
We report the case of a rare anomaly of the right coronary artery (RCA) arising from the left aortic sinus, having a single ostium with the left coronary artery, associated with documented episodes of inferior ischemia, in which surgical treatment with a right internal thoracic artery to RCA bypass graft and the corresponding ligation provided greater stability to the coronary blood flow and good clinical progress.
Asunto(s)
Anomalías de los Vasos Coronarios/diagnóstico , Seno Aórtico/anomalías , Angiografía Coronaria , Puente de Arteria Coronaria , Anomalías de los Vasos Coronarios/cirugía , Vasos Coronarios/cirugía , Electrocardiografía , Humanos , Masculino , Persona de Mediana Edad , Isquemia Miocárdica/diagnóstico , Isquemia Miocárdica/cirugía , Seno Aórtico/cirugíaRESUMEN
Relatamos caso de rara anomalia de coronária direita (CD) originando em seio aórtico esquerdo, óstio único com coronária esquerda, associado a episódios de isquemia inferior documentados, no qual o tratamento cirurgico com ´by pass´ de artéria torácica interna direita para CD com respectiva ligadura proporcionou maior estabilidade ao fluxo coronario com boa evolução clínica.
We report the case of a rare anomaly of the right coronary artery (RCA) arising from the left aortic sinus, having a single ostium with the left coronary artery, associated with documented episodes of inferior ischemia, in which surgical treatment with a right internal thoracic artery to RCA bypass graft and the corresponding ligation provided greater stability to the coronary blood flow and good clinical progress.