Asunto(s)
Dermatosis del Pie/tratamiento farmacológico , Dermatosis del Pie/radioterapia , Dermatosis de la Mano/tratamiento farmacológico , Dermatosis de la Mano/radioterapia , Psoriasis/tratamiento farmacológico , Psoriasis/radioterapia , Terapia Ultravioleta , 5-Metoxipsoraleno/administración & dosificación , Hospitales de Enseñanza , Humanos , Metoxaleno/administración & dosificación , Terapia PUVA , Fármacos Fotosensibilizantes/uso terapéutico , Estudios RetrospectivosAsunto(s)
Trastornos por Fotosensibilidad/epidemiología , Enfermedades Cutáneas Genéticas/epidemiología , Adolescente , Adulto , Edad de Inicio , Niño , Preescolar , Dermatosis Facial/epidemiología , Femenino , Dermatosis de la Mano/epidemiología , Humanos , Lactante , Masculino , Persona de Mediana Edad , Calidad de Vida , Escocia/epidemiología , Distribución por Sexo , Luz Solar/efectos adversos , Factores de Tiempo , Rayos Ultravioleta/efectos adversos , Adulto JovenRESUMEN
Hidradenitis suppurativa (HS) is a chronic relapsing inflammatory disease resulting in subcutaneous abscesses, sinus tracts and scarring, arising predominantly in apocrine gland-bearing skin. The sites affected, in order of frequency, are the axillae, groins, perianal and perineal region, mammary and submammary skin, buttocks, and pubic region. Other sites that may be affected more rarely include the chest, eyelids, scalp, retroauricular and preauricular skin, thighs, and abdomen. Research has suggested that mechanical friction and follicular occlusion is the primary cause of HS. HS is one of the conditions of the 'follicular occlusion tetrad', which share a similar pathogenesis. HS at atypical sites may mimic other conditions both clinically and pathologically, so misdiagnosis is possible. We present a case series that illustrates a range of atypical sites affected. Our patients all had severe disease. Satisfactory control has not been achieved despite years of medical and surgical interventions.