Intrascrotal epidermoid cyst with extension into the pelvis.

An 8-year-old boy presented with an asymptomatic extratesticular, scrotal epidermoid cyst with extension across the urogenital diaphragm into the pelvis. While routine contrast studies and ultrasound were performed, magnetic resonance imaging was most useful in depicting the anatomical boundaries of the lesion, including the intrapelvic extension. Complete excision was performed transcrotally. The lesion is histologically indistinguishable from epidermoid cysts found elsewhere in the external genitalia, that is the penis, scrotum or testis. The etiology is unknown but it may represent a monolayer teratoma of germ cell origin or abnormal embryological closure of the median raphe.

Two-stage repair for severe hypospadias.

In 39 patients a 2-stage modified Belt-Fuqua repair was performed for severe hypospadias and chordee. Patient age at initial surgery averaged 2 years and stage 2 was done 7 months later. Testosterone was given before stage 1 to 22 patients (56%) and before both stages to 13 (33%). Of 5 patients with intersex 2 had mixed gonadal dysgenesis, 1 was a true hermaphrodite and 2 were 46 XX male subjects. The preoperative meatal location was subglanular in 9 cases, mid shaft in 8, proximal shaft in 2, penoscrotal in 15 and perineal in 5. Those with subglanular meatus had hypoplastic distal urethras and severe chordee. A dorsal Nesbit procedure for chordee correction was done in 24 cases (62%). Neourethral length ranged from 3 to 7 cm. (average 4 cm.) and average followup was 16 months. Neourethral diverticula developed in 8 cases (21%) and they were repaired uneventfully an average of 7 months (range 2 to 24) after stage 2. Minor urethral strictures (3 distal and 4 proximal) were treated with a single visual internal urethrotomy and there was 1 (2.5%) urethrocutaneous fistula. All children had excellent cosmetic and functional outcomes. A staged approach allows for cosmetic reconstruction of the glans and mucosal collar during stage 1 and offers 2 opportunities to augment penile size with testosterone. Bladder or buccal mucosal grafts are avoided since the prepuce is always adequate. There are no hypospadias deformities, penile shaft torsion or asymmetry. Fistula formation is minimal and strictures are minor. The 2-stage repair remains a safe, reliable alternative for boys with severe hypospadias.

Current perception threshold. Reproducibility and comparison with nerve conduction in evaluation of carpal tunnel syndrome.

Neuro-selective current perception threshold (CPT) values quantify peripheral nerve (n) integrity and provide an index of adequate hemodialysis (HD). Evaluation of polyneuropathy (PN) by CPT correlates with nerve conduction testing (NCT). CPT is convenient, painless, and may be performed during HD. Early detection of carpal tunnel syndrome (CTS), a complication of uremia, permits curative intervention. Utility of CPT and NCT measurements in detecting CTS in 29 stable HD patients were evaluated. Reproducibility of seven CPT determinations over 4 weeks was determined in each of 9 HD patients. The coefficient of variation for repeated 2000 Hz CPT measures was 6%. PN was detected by CPT in 92% of the patients and by NCT in 79% (r = 0.79, p less than 0.001). In 38% of the hands there was a CPT impairment in both the median and ulnar nerves (n), of which 25% were symptomatic for CTS. CPTs consistent with CTS (sufficiently greater impairment of the median vs ulnar n) were observed in 31% of the hands with combined median and ulnar n CPT abnormalities, and 11% were identified with CTS by NCT. The unique ability of the CPT exam to quantify hyperesthesia may account for its superior CTS detection sensitivity. These findings demonstrate that repeated CPT determinations are consistent and are diagnostic for CTS.