RESUMEN
Madelung disease is rare, and characterised by accumulation of fatty non-encapsulated tissue in the head, neck, shoulders, and upper extremities. The aetiology is not completely known, but the association with alcohol intake is clear. We present a neglected case that was associated with bilateral asymmetrical gynaecomastia. To the best of our knowledge, this is a pattern of involvement not previously reported. The treatment of choice is lipectomy for severe cases and liposuction for less extensive accumulations of fat.
Asunto(s)
Enfermedades de los Genitales Masculinos/diagnóstico , Ginecomastia/diagnóstico , Lipomatosis Simétrica Múltiple/diagnóstico , Escroto/fisiopatología , Alcoholismo/complicaciones , Alcoholismo/diagnóstico , Estudios de Seguimiento , Enfermedades de los Genitales Masculinos/complicaciones , Ginecomastia/complicaciones , Ginecomastia/cirugía , Humanos , Lipectomía/métodos , Lipomatosis Simétrica Múltiple/complicaciones , Lipomatosis Simétrica Múltiple/cirugía , Masculino , Mastectomía/métodos , Persona de Mediana Edad , Enfermedades Raras , Medición de Riesgo , Índice de Severidad de la Enfermedad , Fumar/efectos adversos , Resultado del TratamientoRESUMEN
PURPOSE: This case report describes a rare and aggressive ameloblastic carcinoma that infiltrated the mandible in a "honeycomb" pattern. METHODS: A total mandibulectomy with bilateral modified neck dissection was followed by primary reconstruction with a single free vascularised fibula flap. RESULTS: The postoperative course was uneventful. The one year follow-up revealed no signs of recurrent tumour or metastases. Nine months later distant metastases occurred in the lung. CONCLUSION: Ameloblastic carcinoma is a highly malignant lesion, which requires aggressive therapy. Prognosis is poor. Further reporting of ameloblastic carcinoma is encouraged.
