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1.
Semin Pediatr Neurol ; 49: 101123, 2024 Apr.
Artículo en Inglés | MEDLINE | ID: mdl-38677802

RESUMEN

Acute neuromuscular disorders occasionally occur in the Pediatric Neurologic Intensive Care Unit. Many of these are primary disorders of the motor unit that may present acutely or exacerbate during an intercurrent illness. Additionally, acute neuromuscular disorders may develop during an acute systemic illness requiring intensive care management that predispose the child to another set of acute motor unit disorders. This chapter discusses acute neuromuscular crises in the infant, toddler, and adolescent, as well as neuromuscular disorders resulting from critical illness.


Asunto(s)
Enfermedad Crítica , Enfermedades Neuromusculares , Humanos , Enfermedades Neuromusculares/fisiopatología , Enfermedades Neuromusculares/terapia , Enfermedades Neuromusculares/diagnóstico , Recién Nacido , Niño , Lactante , Preescolar , Adolescente , Unidades de Cuidado Intensivo Pediátrico
2.
Crit Care Clin ; 39(1): 123-138, 2023 Jan.
Artículo en Inglés | MEDLINE | ID: mdl-36333027

RESUMEN

Diseases of the peripheral nervous system create an additional diagnostic conundrum within the intensive care setting. Causes are vast, presentations are myriad, and symptoms are often ill-defined or misidentified. Care benefits from a multidisciplinary approach including a neuromuscular specialist, rehabilitation services, and a specialty pharmacist in addition to the neurocritical care team. In general, survivors achieve a good functional recovery relative to their preintensive care unit baseline.


Asunto(s)
Enfermedades Neuromusculares , Humanos , Enfermedades Neuromusculares/diagnóstico , Enfermedades Neuromusculares/terapia , Cuidados Críticos , Debilidad Muscular/diagnóstico , Debilidad Muscular/etiología , Debilidad Muscular/terapia , Unidades de Cuidados Intensivos , Enfermedad Crítica
3.
Artículo en Chino | WPRIM (Pacífico Occidental) | ID: wpr-990536

RESUMEN

Neuromuscular diseases are a group of disorders that affect the anterior horn cells of the spinal cord, peripheral nerves, neuromuscular junction and skeletal muscle.A subset of children with neuromuscular disease have rapidly progressive conditions that threaten respiratory and medulla oblongata function.The main causes of neuromuscular disease in PICU include severe neurological impairment, infections, comorbidities, unexpected situations, and other conditions that can exacerbate the primary disease.In each case, timely identification and development of the specific therapies and supportive care measures could improve prognosis.

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