RESUMEN
Angiokeratomas are benign tumors characterized by ectasia of blood vessels in the papillary dermis associated with acanthosis and hyperkeratosis of the epidermis. Dermatological examination of angiokeratomas of Fordyce is characterized by papular keratotic lesions of erythematous-violet color. They are more common in the scrotum, and vulvar involvement is rarely reported. Histopathology is particularly important to distinguish them from other benign and malignant tumors. The article reports the case of a middle-aged black woman with a history of chronic constipation, varicose veins of the lower limbs and cesarean section performed 20 years ago who had had multiple vulvar angiokeratomas for three months.
Asunto(s)
Angioqueratoma/diagnóstico , Neoplasias Cutáneas/diagnóstico , Neoplasias de la Vulva/diagnóstico , Angioqueratoma/terapia , Femenino , Humanos , Persona de Mediana Edad , Neoplasias Cutáneas/terapia , Neoplasias de la Vulva/terapiaRESUMEN
Os angioceratomas são tumores benignos caracterizados por ectasia dos vasos sanguíneos da derme papilar associada à acantose e hiperceratose da epiderme. Ao exame dermatológico, os angioceratomas de Fordyce caracterizam-se por lesões papulo-ceratóticas de coloração eritemato-violácea. São mais comuns no escroto, sendo raramente relatada a localização vulvar. A histopatologia é particularmente importante para difer enciá-los de outros tumores benignos e malignos. O artigo relata o caso de uma mulher negra de meia idade com história de obstipação intestinal, varizes de membros inferiores e cesárea há 20 anos que apresentava múltiplos angioceratomas vulvares há três meses.
Angiokeratomas are benign tumors characterized by ectasia of blood vessels in the papillary dermis associated with acanthosis and hyperkeratosis of the epidermis. Dermatological examination of angiokeratomas of Fordyce is characterized by papular keratotic lesions of erythematous-violet color. They are more common in the scrotum, and vulvar involvement is rarely reported. Histopathology is particularly important to distinguish them from other benign and malignant tumors. The article reports the case of a middle-aged black woman with a history of chronic constipation, varicose veins of the lower limbs and cesarean section performed 20 years ago who had had multiple vulvar angiokeratomas for three months.
Asunto(s)
Femenino , Humanos , Persona de Mediana Edad , Angioqueratoma/diagnóstico , Neoplasias Cutáneas/diagnóstico , Neoplasias de la Vulva/diagnóstico , Angioqueratoma/terapia , Neoplasias Cutáneas/terapia , Neoplasias de la Vulva/terapiaRESUMEN
El angioqueratoma nevoide circunscrito es el más raro de los cinco tipos de angioqueratomas descritos en la literatura. Estas lesiones usualmente están presentes al nacimiento y no se relacionan con enfermedad sistémica. Presentamos el caso de un hombre de 32 años con cuadro clínico de angioqueratoma nevoide circunscrito tratado con crioterapia, con buena respuesta inicial.