ABSTRACT
A 37 year-old previously healthy man from Jamaica presented with 2-3 months of progressive trouble ambulating and incontinence. By 1 month prior to arrival he was wheelchair bound and unable to ambulate even with assistance. He started to wear a diaper for bladder and bowel incontinence. He also complained of painless numbness in his legs over the same period of time. His exam is notable for marked weakness and spasticity in his legs, with hyper-reflexia and clonus. He has a sensory level at the level of the umbilicus. An MRI shows a longitudinally extensive T2 signal change throughout the thoracic cord. His cerebrospinal fluid is mildly inflammatory. His HTLV-1 antibody test is reactive.
Subject(s)
HTLV-I Antibodies/urine , Nervous System Diseases/pathology , Spinal Cord Neoplasms/physiopathology , Urinary Incontinence/physiopathology , Adult , Humans , Jamaica , Male , Nervous System Diseases/physiopathology , Spinal Cord/virology , Urinary Incontinence/diagnosisABSTRACT
Os autores relatam o caso de um paciente de 7 anos de idade, com quadro de dor cervical e tetraparesia progressiva há 2 meses, que apresentava lesäo cística intrarraquiana de C4 a C6. Foi submetido a exerese da lesäo por via anterior, através de corporectomia de C5-C6 e reconstruçäo com enxerto de crista ilíaca e placa metálica. O diagnóstico anátomo-patológico da lesäo foi de cisto enterógeno. Aspectos relacionados a apresentaçäo clínica, embriologia e tratamento dessa lesäo säo discutidos.
Subject(s)
Child , Humans , Male , Spina Bifida Occulta/physiopathology , Spinal Cord Neoplasms/physiopathology , Spinal Cord/pathologyABSTRACT
Os autores descrevem um raro caso de hipertensäo intracraniana conseqüente a glioblastoma multiforme situado na medula cervical de uma paciente jovem. Analisam a fisiopatologia de hipertensäo intracraniana em tumores medulares e a raridade desse tipo de tumor nessa localizaçäo, assim como seus aspectos clínico-patológicos