RÉSUMÉ
Behçet's disease is a relapsing, inflammatory, multi-systemic disease. Coronary arterial involvement in Behçet's disease is very rare with a prevalence of less than 0.5%. We report the case of a 34-year-old man who presented with a coronary artery pseudoaneurysm associated with Behçet's disease. The patient underwent a successful left internal thoracic artery to left anterior descending artery bypass graft procedure, and remains symptom-free in a 6-month follow up with normal electrocardiogram.
Sujet(s)
Faux anévrisme , Maladie de Behçet , Adulte , Faux anévrisme/imagerie diagnostique , Faux anévrisme/étiologie , Faux anévrisme/chirurgie , Maladie de Behçet/complications , Maladie de Behçet/diagnostic , Maladie de Behçet/traitement médicamenteux , Vaisseaux coronaires/imagerie diagnostique , Humains , MâleRÉSUMÉ
A metastatic synovial sarcoma in the right atrium and ventricle is described. A 36-year-old man was admitted to our hospital with generalized fatigue, dyspnoea, and precordial pain. Transthoracic echocardiography demonstrated a metastatic tumour in both the right atrium and right ventricle and revealed obstruction of the inflow tract of the right ventricle caused by a metastatic right atrial tumour. Thoracic computed tomography revealed a pleural-based paravertebral mass in the left intrathoracic cavity and multiple pulmonary nodules in both lungs. Cardiac surgery was performed for palliative treatment due to right cardiac failure and a risk of fatal embolization. The patient died 12 months after the cardiac surgery.
Sujet(s)
Atrium du coeur/anatomopathologie , Tumeurs du coeur/anatomopathologie , Ventricules cardiaques/anatomopathologie , Sarcome synovial/anatomopathologie , Adulte , Échocardiographie , Issue fatale , Tumeurs du coeur/imagerie diagnostique , Tumeurs du coeur/chirurgie , Humains , Mâle , Sarcome synovial/imagerie diagnostique , Sarcome synovial/chirurgie , TomodensitométrieRÉSUMÉ
Thrombus in sinus of Valsalva is unusual reason for acute myocardial infarction. We demonstrated a case with floating thrombus in sinus of Valsalva obstructing the right coronary ostium intermittently, and causing cardiogenic shock. The patient was diagnosed with multiplane transesophageal echocardiography and treated successfully with surgical removal of mass. A homozygote polymorphism of plasminogen activator inhibitor (PAI) 1 4G/5G was found. This is the first report demonstrating a patient with PAI 1 polymorphism and thrombus of Valsalva complicated with cardiogenic shock.
