RÉSUMÉ
INTRODUCTION: The association granulomatosis - combined variable immunodeficiency (CVID) - is well known from the clinicians. However, the association with a large granular lymphocyte (LGL) leukemia has not been yet reported. CASE REPORT: We report a 50-year-old woman, followed for CVID associated with a granulomatous disease. During the follow-up, the patient developed a granulomatous lymphocytic interstitiel lung disease (GLILD). Secondarily, she presented a LGL leukemia. CONCLUSION: To our knowledge, this is the first reported case of an association between CVID and LGL leukemia.
Sujet(s)
Déficit immunitaire commun variable/complications , Granulome/étiologie , Pneumopathies interstitielles/étiologie , Déficit immunitaire commun variable/imagerie diagnostique , Déficit immunitaire commun variable/anatomopathologie , Femelle , Granulome/imagerie diagnostique , Granulome/anatomopathologie , Humains , Pneumopathies interstitielles/imagerie diagnostique , Pneumopathies interstitielles/anatomopathologie , Adulte d'âge moyen , Radiographie thoraciqueRÉSUMÉ
We report the case of a 51-year-old man who presents with worsening dyspnea at exercise caused by a large thymic lipoma (6 kg). We present the clinical, radiological, and spiral CT scan features of this rare and benign tumor and correlate them with the pathologic findings.