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Indian J Pathol Microbiol
; 64(2): 373-375, 2021.
Article
de Anglais
| MEDLINE
| ID: mdl-33851638
RÉSUMÉ
Malignant gastrointestinal neuroectodermal tumor (GNET) is a rare neoplasm with unknown etiology. It was previously referred to as Clear cell sarcoma of gastrointestinal tract. This tumor is characterized by a higher rate of local recurrence and metastasis. Due to its aggressive clinical course, distinguishing this entity from various other mimickers is very essential. Herein, we present a case of malignant GNET in a 33-year-old male patient.
Sujet(s)
Tumeurs gastro-intestinales/diagnostic , Tumeurs gastro-intestinales/anatomopathologie , Tube digestif/anatomopathologie , Tumeurs neuroectodermiques/diagnostic , Tumeurs neuroectodermiques/anatomopathologie , Adulte , Marqueurs biologiques tumoraux , Tumeurs gastro-intestinales/génétique , Tumeurs gastro-intestinales/thérapie , Humains , Immunohistochimie/méthodes , Hybridation fluorescente in situ , Mâle , Tumeurs neuroectodermiques/génétique , Tumeurs neuroectodermiques/thérapie , Protéine EWS de liaison à l'ARN/génétique , Sarcome à cellules claires/anatomopathologie
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