ABSTRACT
We present a case of a premature infant with a presumed obstructive uropathy found to be a megalourethra leading to a perinatal postrenal failure. A megalourethra - an uncommon cause of urethral dilatation - is a congenital, non-obstructive anomaly of the penile erectile tissue. We think that a distal stenosis resulted in dysplasia of the penile tissue and an aspect of a megalourethra. Further diagnostic workup included urinary tract sonograms, a voiding cystourethrogram and MAG3 scintigrafy. Initially the patient was managed with supportive care such as a suprapubic urinary catheter, followed by surgical intervention (Bengt Johanson).
Subject(s)
Infant, Premature, Diseases/etiology , Perinatal Care , Renal Insufficiency/etiology , Urethra/abnormalities , Dilatation, Pathologic/congenital , Dilatation, Pathologic/diagnosis , Dilatation, Pathologic/surgery , Follow-Up Studies , Humans , Infant , Infant, Newborn , Infant, Premature, Diseases/diagnosis , Male , Renal Insufficiency/diagnosis , Renal Insufficiency/surgery , Technetium Tc 99m Mertiatide , Urethra/surgery , Urinary Bladder/abnormalities , Urinary Retention/diagnosis , Urinary Retention/etiology , UrographyABSTRACT
We report a 12-year-old girl with a long history of constant urinary dribbling and apparently only a left kidney. Using a multimodality approach involving the fusion of MR urography and (99m)Tc-dimercaptosuccinic acid (DMSA) SPECT datasets, it was finally possible to exactly localize the very small dystopic, dysplastic right kidney and its ectopic ureter draining into the vagina.