[Syndrome of left heart hypoplasia, causing hydrops fetalis and congenital pulmonary lymphangiectasis]. / Síndrome del corazón izquierdo hipoplásico, debutando como hydrops fetalis y linfangiectasia pulmonar congénita.

A case of hydrops fetalis and congenital pulmonary lymphangiectasis due to hypoplastic left heart syndrome with intact atrial septum is reported. Authors analyse hydrops and lymphangiectasis physiology in relation to cardiac defect, besides the present day therapeutics possibilities. Patient died four hours after birth.