RESUMO
Congenital granular cell myoblastoma of the newborn is a rare tumor. The combination of polyhydramnios caused by obstruction of the infant's mouth by this tumor is extremely rare, and this is the first published report of such a condition.
Assuntos
Neoplasias Maxilomandibulares/embriologia , Neoplasias de Tecido Muscular/embriologia , Poli-Hidrâmnios/complicações , Adulto , Processo Alveolar/patologia , Feminino , Humanos , Recém-Nascido , Neoplasias Maxilomandibulares/patologia , Neoplasias Maxilomandibulares/cirurgia , Neoplasias de Tecido Muscular/patologia , Neoplasias de Tecido Muscular/cirurgia , GravidezRESUMO
Three cases of granular cell myoblastoma have been studied in order to determine the presence and distribution of the S-100 specific protein in the neoplastic cells, using immunocytochemical staining techniques, through the modified avidin-biotin method. Positive immunostaining was observed in the three cases studied. The comparative study of various control cases histogenetically originating from neuroectoderm (melanoma) and specifically from Schwann cells, as also the presence of strongly positive staining in Schwann cells of peripheral nerve fibres situated inside and outside the tumor, support the concept of the neurogenic origin of this interesting tumor.