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MCN Am J Matern Child Nurs
; 19(3): 162-4, 1994.
Artigo
em Inglês
| MEDLINE
| ID: mdl-8028455
2.
J Neurosci Nurs
; 18(3): 146-9, 1986 Jun.
Artigo
em Inglês
| MEDLINE
| ID: mdl-2941501
RESUMO
Steely hair disease, a neurodegenerative disorder, is characterized by slow growth, progressive cerebral dysfunction, kinky friable hair, x-linked inheritance, and death before three years of age. Low-serum copper has been found to play a role in steely hair disease. This article describes the role of copper, the pathophysiology of this disease, and current treatment and research. A case history and pertinent aspects of nursing care of these patients are also presented.