[Intra-abdominal desmoplastic small round cell tumor in childhood: case report and review of the literature]. / Tumeur desmoplastique à petites cellules rondes intra-abdominale de l'enfant : à propos d'une observation et revue de la littérature.
Bull Cancer
; 90(12): 1063-6, 2003 Dec.
Article
in Fr
| MEDLINE
| ID: mdl-14715426
ABSTRACT
Desmoplastic small round cell tumor (DSRCT) correspond to a recent clinicopathological entity, individualized in 1989 into the group of tumors with small round cells. This pathology puts ethiopathogenic, diagnostic, therapeutic and prognosis problems. Indeed, the ethiopathogenic is still unknown, diagnosis is asserted only by immuno-histochimic and cytogenetic study because of the big number of differential diagnoses and the anatomopathologic polymorphism. Its treatment is not well codified and its outcome remains dark in spite of therapeutic progress. The objective of this work is to report a personal observation of a DSRCT and to proceed to a review of the literature to clarify the epidemiological, clinical, paraclinical and therapeutic aspects of this rare tumor.
Search on Google
Collection:
01-internacional
Database:
MEDLINE
Main subject:
Sarcoma, Small Cell
/
Abdominal Neoplasms
Limits:
Child
/
Humans
/
Male
Language:
Fr
Journal:
Bull Cancer
Year:
2003
Document type:
Article
Affiliation country: